{"id":"W1505305037","doi":"10.1007/8904_2012_171","title":"Barriers to Transplantation in Adults with Inborn Errors of Metabolism","year":2012,"lang":"en","type":"article","venue":"JIMD Reports","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":3,"is_retracted":false,"has_abstract":false,"ca_institutions":"Mount Sinai Hospital; University of British Columbia; University Health Network","funders":"","keywords":"Transplantation; Decompensation; Medicine; Inborn error of metabolism; Disease; Organ transplantation; Pediatrics; Intensive care medicine; Surgery; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.003218341,0.00009979091,0.0002722782,0.0002926437,0.001147949,0.001701789,0.0004717463,0.0008008743,0.01170234],"category_scores_gemma":[0.01211157,0.00008270377,0.0001890012,0.0002521144,0.0006154026,0.0008131252,0.001390474,0.001400406,0.001410837],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003720123,"about_ca_system_score_gemma":0.00150454,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009400854,"about_ca_topic_score_gemma":0.001481207,"domain_scores_codex":[0.9989085,0.0004502038,0.0001104516,0.00006284697,0.0002148765,0.000253163],"domain_scores_gemma":[0.9932591,0.00337493,0.001006306,0.0002506106,0.0005242232,0.001584881],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001154906,0.0008905456,0.4744269,0.0005188031,0.00008176499,0.02237088,0.01091462,0.0004108119,0.005698978,0.03896406,0.05704865,0.387519],"study_design_scores_gemma":[0.0001823028,0.002687801,0.3870683,0.004455719,0.0002844181,0.1839463,0.03335553,0.001563858,0.006752485,0.0599187,0.3196768,0.0001077371],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.8430501,0.02341576,0.005937543,0.0564968,0.001220858,0.0001105991,0.0002585838,0.0002156261,0.06929417],"genre_scores_gemma":[0.9810782,0.004724203,0.002527537,0.006383199,0.0006875045,0.0000547542,0.0001209984,0.00005142808,0.004372166],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01170234,"threshold_uncertainty_score":0.03914821,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003438934075746193,"score_gpt":0.2203162977357007,"score_spread":0.2168773636599545,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}