{"id":"W1505305037","doi":"10.1007/8904_2012_171","title":"Barriers to Transplantation in Adults with Inborn Errors of Metabolism","year":2012,"lang":"en","type":"article","venue":"JIMD Reports","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":3,"is_retracted":false,"has_abstract":false,"ca_institutions":"Mount Sinai Hospital; University of British Columbia; University Health Network","funders":"","keywords":"Transplantation; Decompensation; Medicine; Inborn error of metabolism; Disease; Organ transplantation; Pediatrics; Intensive care medicine; Surgery; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002241099,0.0001039676,0.0001480966,0.00006712319,0.00001675457,0.000003105718,0.00005295128,0.00007196936,0.00003884335],"category_scores_gemma":[0.00006408391,0.00008608832,0.00003794815,0.0001426392,0.00003247224,0.00000514361,0.00001493834,0.00003650612,0.000001529626],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000001371758,"about_ca_system_score_gemma":0.00006895883,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00009481177,"about_ca_topic_score_gemma":0.0001799326,"domain_scores_codex":[0.99916,0.00003224588,0.0002572655,0.0002024248,0.000139612,0.0002084677],"domain_scores_gemma":[0.9994224,0.000002712949,0.00009795398,0.000255901,0.00004096754,0.0001800579],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0009258425,0.0001744925,0.7978492,0.0002077,0.0000982564,0.00006873166,0.005466047,0.0008271205,0.1845981,0.0001227794,0.001220783,0.008440977],"study_design_scores_gemma":[0.0009517203,0.0001286924,0.6757858,0.00005866015,0.00006769257,0.0001318614,0.0008265508,0.00000332908,0.2826816,0.0000352173,0.03901037,0.0003184832],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9960777,0.001087929,0.0004016488,0.00004805166,0.0002115048,0.0002175994,0.000007593968,0.000004194455,0.001943828],"genre_scores_gemma":[0.9982676,0.0001447389,0.001129347,0.0001513418,0.00006549899,0.00002998245,0.00005399249,0.00001363659,0.0001438963],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1220633,"threshold_uncertainty_score":0.351058,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003438934075746193,"score_gpt":0.2203162977357007,"score_spread":0.2168773636599545,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}