{"id":"W1552402707","doi":"10.1002/ddrr.1113","title":"Peroxisome biogenesis disorders: Biological, clinical and pathophysiological perspectives","year":2013,"lang":"en","type":"review","venue":"Developmental Disabilities Research Reviews","topic":"Peroxisome Proliferator-Activated Receptors","field":"Biochemistry, Genetics and Molecular Biology","cited_by":160,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital","funders":"","keywords":"Biogenesis; Peroxisomal disorder; Pathophysiology; Medicine; Bioinformatics; Peroxisome; Biology; Neuroscience; Genetics; Pathology; Gene","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","sts","insufficient_payload"],"consensus_categories":[],"category_scores_codex":[0.002651611,0.0009906257,0.002773125,0.0002305274,0.000443552,0.0001874989,0.0009970232,0.001253958,0.0007170366],"category_scores_gemma":[0.006068685,0.0006314482,0.001044586,0.0005734572,0.004361657,0.00002409635,0.001828209,0.001132677,0.0009539363],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002227099,"about_ca_system_score_gemma":0.0005077579,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00002294989,"about_ca_topic_score_gemma":0.000009959209,"domain_scores_codex":[0.9896942,0.004849149,0.001740115,0.002135467,0.0004642931,0.001116736],"domain_scores_gemma":[0.9975947,0.0006242719,0.0002718275,0.0008001707,0.0001904034,0.0005186301],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00002768943,0.0004582551,0.0009164969,0.004552895,0.0002640815,0.000001038155,0.0001887139,6.912098e-9,0.0008774444,0.00008682269,0.008418081,0.9842085],"study_design_scores_gemma":[0.0001814541,0.0005703065,0.00008120155,0.001454048,0.00003849455,0.0000247742,0.00251188,1.701119e-7,0.00007333785,0.0001325243,0.9941244,0.0008074141],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.01829457,0.9768887,0.000003990481,0.00004104101,0.0001687818,0.003803885,0.0001579576,0.00004032081,0.0006007715],"genre_scores_gemma":[0.000319123,0.9925879,0.001446946,0.00004379567,0.0005148852,0.003312994,0.000728456,0.0001015592,0.0009442917],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.9857063,"threshold_uncertainty_score":0.9998239,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.2871536307971279,"score_gpt":0.4634466014174511,"score_spread":0.1762929706203233,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}