{"id":"W1552402707","doi":"10.1002/ddrr.1113","title":"Peroxisome biogenesis disorders: Biological, clinical and pathophysiological perspectives","year":2013,"lang":"en","type":"review","venue":"Developmental Disabilities Research Reviews","topic":"Peroxisome Proliferator-Activated Receptors","field":"Biochemistry, Genetics and Molecular Biology","cited_by":160,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital","funders":"","keywords":"Biogenesis; Peroxisomal disorder; Pathophysiology; Medicine; Bioinformatics; Peroxisome; Biology; Neuroscience; Genetics; Pathology; Gene","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003617409,0.0008075694,0.001235421,0.002441057,0.0003228342,0.0008773358,0.0006376244,0.0009079315,0.004246559],"category_scores_gemma":[0.0004928095,0.0001956426,0.0004057126,0.002365407,0.0005201455,0.001215511,0.0005421984,0.001538943,0.002344192],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005620391,"about_ca_system_score_gemma":0.0009264369,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001042949,"about_ca_topic_score_gemma":0.00176495,"domain_scores_codex":[0.9998325,0.00002958753,0.00002751588,0.00002941501,0.00006284365,0.00001812106],"domain_scores_gemma":[0.9997681,0.00009611648,0.00002980735,0.000007377336,0.0000732113,0.00002546003],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00008804938,0.00006708429,0.0002945933,0.01342362,0.00007389124,0.0008111033,0.0000894281,0.0002181713,0.002766647,0.004363419,0.03287087,0.9449331],"study_design_scores_gemma":[0.00001790448,0.00006326104,0.001159853,0.003362193,0.0001033964,0.006740766,0.0001128884,0.00005822469,0.0005032081,0.003132342,0.9847253,0.00002073704],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00009809104,0.9982989,0.00009249728,0.0003181334,0.0001589567,0.000002176,0.00001198163,0.000006725589,0.001012565],"genre_scores_gemma":[0.0006456249,0.9983138,0.0001500138,0.0001522046,0.0001721607,0.000003633008,0.0000224245,0.000001021844,0.0005390282],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.004246559,"threshold_uncertainty_score":0.01420617,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.2871536307971279,"score_gpt":0.4634466014174511,"score_spread":0.1762929706203233,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}