{"id":"W1578438653","doi":"10.1111/j.1468-1331.2012.03669.x","title":"Cognitive and affective impairments of a novel SCA/MND crossroad mutation Asidan","year":2012,"lang":"en","type":"article","venue":"European Journal of Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":39,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Ministry of Health, Labour and Welfare","keywords":"Montreal Cognitive Assessment; Apathy; Spinocerebellar ataxia; Medicine; Dementia; Ataxia; Depression (economics); Cognition; Cerebellar ataxia; Executive functions; Cognitive decline; Audiology; Psychiatry; Pediatrics; Disease; Internal medicine","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004752049,0.000166969,0.0002467309,0.0001878121,0.0000864351,0.00002266982,0.0001769728,0.00002134144,0.00002025889],"category_scores_gemma":[0.001515292,0.0001470341,0.00008723148,0.0001615049,0.0003650641,0.0002444583,0.0001118701,0.0002476098,0.00001370448],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000006606305,"about_ca_system_score_gemma":0.00003566561,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":8.774243e-7,"about_ca_topic_score_gemma":3.681852e-7,"domain_scores_codex":[0.9973208,0.001487915,0.0004166539,0.0002292416,0.00025023,0.0002951737],"domain_scores_gemma":[0.998431,0.0004821558,0.0005955916,0.0001075002,0.0001689325,0.0002148011],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0007852963,0.0007642749,0.02280564,0.00001866139,0.0000257151,0.0004565124,0.001497287,0.0001086138,0.9686266,0.00007901388,0.00008511361,0.004747333],"study_design_scores_gemma":[0.002814194,0.003288022,0.6113442,0.00002295264,0.00007330484,0.002851201,0.00007778667,0.00007833725,0.3791833,0.00002597155,0.0001062525,0.0001344285],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9968412,0.0001225978,0.001400504,0.0001546762,0.0004378278,0.0001675686,0.00002865509,0.000009075782,0.0008379095],"genre_scores_gemma":[0.9984903,0.00002628336,0.0001290147,0.00112972,0.0001716013,0.000001210427,5.775697e-7,0.0000328029,0.00001843855],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.5894432,"threshold_uncertainty_score":0.5995876,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03654810190099086,"score_gpt":0.2969984649881715,"score_spread":0.2604503630871806,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}