{"id":"W1603975691","doi":"10.1212/wnl.82.10_supplement.p2.184","title":"Mild Case of Unverricht-Lundborg Disease (ULD) Mimicking Juvenile Myoclonic Epilepsy (JME) in Adulthood (P2.184)","year":2014,"lang":"en","type":"article","venue":"Neurology","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Neurological Institute and Hospital","funders":"","keywords":"Juvenile myoclonic epilepsy; Progressive myoclonus epilepsy; Myoclonus; Medicine; Juvenile; Epilepsy; Myoclonic Jerk; Pediatrics; Psychiatry; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001253932,0.001182711,0.0004258935,0.0008063779,0.0007047632,0.0004549931,0.0004035819,0.001388524,0.00176302],"category_scores_gemma":[0.001117701,0.0004406363,0.0003257568,0.000634305,0.0005639841,0.0004894168,0.0008467283,0.0007377997,0.0006117384],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004102834,"about_ca_system_score_gemma":0.0003326125,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001831869,"about_ca_topic_score_gemma":0.003616082,"domain_scores_codex":[0.9998015,0.0000169705,0.00001958572,0.00006005244,0.00002329795,0.00007870494],"domain_scores_gemma":[0.9995298,0.00010458,0.0001162676,0.00003230757,0.00002578199,0.0001913119],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00007857787,0.00002433781,0.01670842,0.00003735591,0.000006745422,0.9771317,0.0002124755,0.00006136376,0.003924276,0.000127977,0.000234848,0.001451875],"study_design_scores_gemma":[0.00001392415,0.0001533061,0.03086874,0.000009052374,0.000007046448,0.9674367,0.00008172046,0.0001112931,0.0005760507,0.00009808382,0.0006355504,0.00000848637],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9937161,0.0008849893,0.0008315069,0.0004283146,0.00005950347,0.00004488808,0.0002787227,0.00008717023,0.003669008],"genre_scores_gemma":[0.9981835,0.0002746155,0.0004380932,0.0001479181,0.00005117302,0.000008246942,0.0001049581,0.0000102594,0.0007811959],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001831869,"threshold_uncertainty_score":0.00589788,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01203484855441924,"score_gpt":0.2621854899648474,"score_spread":0.2501506414104282,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}