{"id":"W1603975691","doi":"10.1212/wnl.82.10_supplement.p2.184","title":"Mild Case of Unverricht-Lundborg Disease (ULD) Mimicking Juvenile Myoclonic Epilepsy (JME) in Adulthood (P2.184)","year":2014,"lang":"en","type":"article","venue":"Neurology","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Neurological Institute and Hospital","funders":"","keywords":"Juvenile myoclonic epilepsy; Progressive myoclonus epilepsy; Myoclonus; Medicine; Juvenile; Epilepsy; Myoclonic Jerk; Pediatrics; Psychiatry; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0002069936,0.0002669792,0.0006185598,0.00027895,0.00006552671,0.000007221107,0.0001636907,0.0001838331,0.0002584172],"category_scores_gemma":[0.0004000703,0.0002581222,0.0002210328,0.0003250356,0.0001417534,0.00006269831,0.0001041709,0.0004108953,0.00008159412],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003069501,"about_ca_system_score_gemma":0.0001808674,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007057071,"about_ca_topic_score_gemma":0.0003058914,"domain_scores_codex":[0.9978843,0.0002450906,0.0005426774,0.0005692089,0.0001990778,0.0005595901],"domain_scores_gemma":[0.9983413,0.000198808,0.0001905882,0.0006861332,0.0001080398,0.0004751489],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.01610501,0.003866964,0.6416419,0.001815666,0.0002972501,0.2876041,0.00154572,0.0006226278,0.008083767,0.004725753,0.01026433,0.02342691],"study_design_scores_gemma":[0.03811403,0.0112773,0.740957,0.0005681441,0.002946139,0.04188258,0.0003145433,0.02798427,0.002135248,0.0022063,0.1294495,0.002164878],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9950406,0.001173538,0.00007776129,0.00191357,0.0005357061,0.0004251052,0.00004322274,0.0000685318,0.0007219752],"genre_scores_gemma":[0.9938885,0.00009566992,0.0001163718,0.005457133,0.000233672,0.00004082842,0.00004412623,0.00005416531,0.00006954248],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2457215,"threshold_uncertainty_score":0.9999871,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01203484855441924,"score_gpt":0.2621854899648474,"score_spread":0.2501506414104282,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}