{"id":"W178339509","doi":"","title":"Metabolic epilepsies: approaches to a diagnostic challenge.","year":2009,"lang":"en","type":"article","venue":"PubMed","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":10,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"","keywords":"Epilepsy; Myoclonic epilepsy; Medicine; Ketogenic diet; Progressive myoclonus epilepsy; Neuronal ceroid lipofuscinosis; Pediatrics; Metabolic disorder; Internal medicine; Disease; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00193783,0.0009393454,0.001492049,0.003156647,0.0005455703,0.002021497,0.001334802,0.00273343,0.005030816],"category_scores_gemma":[0.005220289,0.0003317682,0.0005825751,0.001399141,0.001600468,0.005357817,0.001842252,0.005096524,0.003976007],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001180379,"about_ca_system_score_gemma":0.001894092,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001928306,"about_ca_topic_score_gemma":0.003053457,"domain_scores_codex":[0.9993497,0.0001731822,0.0001208013,0.00008988121,0.0001993505,0.00006721739],"domain_scores_gemma":[0.9971386,0.001326754,0.0001791841,0.0001336912,0.0008744865,0.0003472819],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00008052,0.00004746849,0.002152775,0.002822875,0.00006644868,0.009392423,0.00033903,0.0002399833,0.001115424,0.01611407,0.2425254,0.7251036],"study_design_scores_gemma":[0.00003570531,0.00007391238,0.002301084,0.006069876,0.00009355384,0.08883291,0.0009911479,0.0004011312,0.0002922816,0.0421771,0.8586671,0.00006418863],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"other","genre_scores_codex":[0.0007962164,0.9344612,0.00384353,0.05073522,0.003905416,0.00001570808,0.0001495515,0.0001744881,0.005918649],"genre_scores_gemma":[0.009086897,0.9410992,0.0097037,0.01922784,0.01649408,0.00004662929,0.0005368512,0.00007327434,0.003731532],"genre_candidate":"other","genre_consensus":null,"teacher_disagreement_score":0.005030816,"threshold_uncertainty_score":0.01682973,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05016140773168942,"score_gpt":0.2183902404119165,"score_spread":0.168228832680227,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}