{"id":"W1901020598","doi":"10.1002/pbc.25756","title":"Successful Allogeneic Hematopoietic Stem Cell Transplantation in XIAP Deficiency Using Reduced‐Intensity Conditioning","year":2015,"lang":"en","type":"article","venue":"Pediatric Blood & Cancer","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":20,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Hemophagocytic lymphohistiocytosis; XIAP; Hematopoietic stem cell transplantation; Stem cell; Transplantation; Oncology; Immunology; Haematopoiesis; Salvage therapy; Internal medicine; Apoptosis; Chemotherapy; Disease; Programmed cell death; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001980246,0.0005606152,0.0004578958,0.0003272865,0.0005886118,0.0002907776,0.0002761758,0.0005977181,0.0004466723],"category_scores_gemma":[0.0004791892,0.0001445869,0.0004771347,0.0002153841,0.0004614717,0.0002519579,0.00048014,0.0009564998,0.0002382176],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002597467,"about_ca_system_score_gemma":0.00046016,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0003785221,"about_ca_topic_score_gemma":0.0005306962,"domain_scores_codex":[0.999881,0.00002022902,0.00001789842,0.00002528119,0.00001964304,0.00003594511],"domain_scores_gemma":[0.9998255,0.00004325037,0.00003616568,0.00002146943,0.000006599842,0.00006709008],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0006326788,0.0009176265,0.05245087,0.0002459968,0.0001084808,0.824512,0.0006787947,0.002026097,0.05168821,0.001937413,0.001804354,0.06299755],"study_design_scores_gemma":[0.0001796224,0.002092327,0.03013405,0.0000473986,0.0001227675,0.9327115,0.0001328006,0.002446986,0.02649933,0.0007985404,0.004810775,0.00002375994],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9853725,0.001906369,0.006625108,0.0008747591,0.0001253593,0.000113114,0.0001069467,0.0001764714,0.004699463],"genre_scores_gemma":[0.9970905,0.000761351,0.001244412,0.0001996682,0.00008195172,0.00001884736,0.00009053899,0.00002294071,0.0004897982],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0005977181,"threshold_uncertainty_score":0.00188458,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03910242246971331,"score_gpt":0.3064017909397315,"score_spread":0.2672993684700182,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}