{"id":"W1946126563","doi":"10.1111/j.1542-4758.2011.00591.x","title":"Coma, hyperammonemia, metabolic acidosis, and mutation: Lessons learned in the acute management of late onset urea cycle disorders","year":2011,"lang":"en","type":"article","venue":"Hemodialysis International","topic":"Metabolism and Genetic Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":11,"is_retracted":false,"has_abstract":true,"ca_institutions":"London Health Sciences Centre; Western University","funders":"","keywords":"Hyperammonemia; Urea cycle; Medicine; Coma (optics); Metabolic acidosis; Acidosis; Metabolic disorder; Urea; Intensive care medicine; Hemodialysis; Pediatrics; Internal medicine; Genetics; Biochemistry; Arginine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001920075,0.001261931,0.001395959,0.000942483,0.0005907217,0.001582227,0.00166138,0.005031765,0.001209038],"category_scores_gemma":[0.005313321,0.0003605924,0.0008818662,0.0003885401,0.001604287,0.003519528,0.001111031,0.00738455,0.0006873554],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001191361,"about_ca_system_score_gemma":0.001340128,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003185351,"about_ca_topic_score_gemma":0.004276949,"domain_scores_codex":[0.9992786,0.0002431473,0.0001486455,0.00008426781,0.0001353157,0.00011002],"domain_scores_gemma":[0.9976191,0.001181499,0.0001684726,0.0001155612,0.0003916679,0.0005237458],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"case_report","study_design_scores_codex":[0.0005773521,0.001158279,0.02659685,0.001925488,0.0002333904,0.1044358,0.001313675,0.002898858,0.003266298,0.008329116,0.08532789,0.7639369],"study_design_scores_gemma":[0.001322126,0.003720359,0.0627167,0.01191837,0.0008182894,0.4580207,0.01043546,0.01619313,0.005939461,0.1007205,0.3274067,0.0007881789],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"review","genre_gemma":"empirical","genre_scores_codex":[0.08917659,0.4582138,0.04586565,0.3693944,0.01341021,0.0002797634,0.0002253768,0.0009669753,0.02246723],"genre_scores_gemma":[0.4110183,0.4173097,0.05427549,0.05561074,0.054665,0.0003275156,0.0003030284,0.0001976045,0.006292558],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.005031765,"threshold_uncertainty_score":0.01015443,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01859262763657709,"score_gpt":0.2771504212158313,"score_spread":0.2585577935792542,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}