{"id":"W1955161220","doi":"10.3233/jnd-140025","title":"DM1 Patients with Small CTG Expansions are also at Risk of Severe Conduction Abnormalities","year":2015,"lang":"en","type":"article","venue":"Journal of Neuromuscular Diseases","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":5,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Sherbrooke; Cégep de Jonquière; Cégep de Chicoutimi","funders":"Canadian Institutes of Health Research; Muscular Dystrophy Canada","keywords":"Medicine; Internal medicine; Cardiology; Myotonic dystrophy; QRS complex; Abnormality; Electrocardiography; Atrial flutter; Atrial fibrillation; PR interval; Conduction abnormalities; Atrioventricular block; Heart rate; Blood pressure","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003667264,0.0004367208,0.0003376556,0.0004317198,0.000392987,0.0004398031,0.0002249809,0.000425424,0.001935055],"category_scores_gemma":[0.001470328,0.0001388109,0.0003503995,0.0004678731,0.0002026178,0.0002656423,0.0002900018,0.0005828284,0.0002627777],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001203999,"about_ca_system_score_gemma":0.0001357343,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009799359,"about_ca_topic_score_gemma":0.001269131,"domain_scores_codex":[0.9997602,0.0000623969,0.00002606727,0.0000616027,0.00004196127,0.00004776158],"domain_scores_gemma":[0.9984424,0.0003377717,0.0008965197,0.00004551253,0.00008157437,0.0001963483],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000179134,0.00001320638,0.997271,0.000007579123,0.00003310519,0.0004266759,0.00002126315,0.00004131462,0.0004378294,0.000009344662,0.00004705969,0.001512448],"study_design_scores_gemma":[0.000008407321,0.0001391175,0.9950849,0.000009620435,0.00005512681,0.004045402,0.00006242255,0.0002253776,0.0001715832,0.00002929508,0.0001651592,0.00000364935],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9991622,0.0003664036,0.00009443992,0.00004095378,0.000005249167,0.000002619096,0.00006943716,0.000004519699,0.0002542091],"genre_scores_gemma":[0.9994801,0.00009638395,0.0001146991,0.00002351517,0.00002069609,0.00000218432,0.0001434164,0.000001571984,0.0001174575],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001935055,"threshold_uncertainty_score":0.006473422,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04085095963347729,"score_gpt":0.2387092342620639,"score_spread":0.1978582746285867,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}