{"id":"W1964424631","doi":"10.1016/j.brainres.2003.11.067","title":"Late onset Tay–Sachs disease in mice with targeted disruption of the Hexa gene: behavioral changes and pathology of the central nervous system","year":2004,"lang":"en","type":"article","venue":"Brain Research","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":34,"is_retracted":false,"has_abstract":false,"ca_institutions":"Montreal Children's Hospital; McGill University; University of Lethbridge; University of Calgary","funders":"Canadian Institutes of Health Research","keywords":"HEXA; Central nervous system; Neuroscience; Pathology; Nervous system; Disease; Medicine; Anatomy; Biology","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008999152,0.0001204083,0.000252955,0.0001906949,0.0001266932,0.00001410327,0.0003041176,0.00009712401,0.00001306471],"category_scores_gemma":[0.0003436415,0.00006660922,0.00005663478,0.0008576236,0.000800929,0.00004097584,0.0002689922,0.0004904255,0.0000018983],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002159434,"about_ca_system_score_gemma":0.000446319,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003614688,"about_ca_topic_score_gemma":0.002310627,"domain_scores_codex":[0.9972276,0.0007274835,0.0002148391,0.0002961248,0.0009626895,0.0005712542],"domain_scores_gemma":[0.998919,0.0001278656,0.00006986217,0.0004731735,0.0002316005,0.0001784853],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00240446,0.0008289515,0.8629327,0.0011324,0.00004153262,0.0006710635,0.00372163,0.0002185775,0.1249866,0.0002454905,0.0001329844,0.002683595],"study_design_scores_gemma":[0.002145712,0.000445629,0.9868693,0.0003651925,0.00002297837,0.00007313965,0.001089612,0.0001883131,0.008645049,0.00005118045,0.00003250182,0.0000713705],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9901762,0.0008408665,0.000006784678,0.007414488,0.00003595949,0.001391196,0.00008311313,0.00001133882,0.00004003335],"genre_scores_gemma":[0.9994077,0.00004776682,0.00004671125,0.00004988447,0.00002905143,0.00007667584,0.00001686984,0.00002379225,0.0003015155],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1239366,"threshold_uncertainty_score":0.5464351,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04017000941782791,"score_gpt":0.3423314168711725,"score_spread":0.3021614074533446,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}