{"id":"W1964630210","doi":"10.1002/pbc.22061","title":"Dyskeratosis congenita: The first NIH clinical research workshop","year":2009,"lang":"en","type":"article","venue":"Pediatric Blood & Cancer","topic":"Telomeres, Telomerase, and Senescence","field":"Medicine","cited_by":69,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia; Terry Fox Research Institute","funders":"National Cancer Institute; National Institutes of Health","keywords":"Dyskeratosis congenita; Medicine; Telomere; Bone marrow failure; Stem cell; Blood cancer; Cancer; Gene; Internal medicine; Genetics; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.009389076,0.001074779,0.0007300162,0.001746465,0.001660439,0.003499472,0.001563838,0.006736031,0.01122737],"category_scores_gemma":[0.006394974,0.0004797365,0.0008732616,0.0006658159,0.0007664228,0.001603451,0.002888641,0.005738636,0.005101473],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.003756379,"about_ca_system_score_gemma":0.007477452,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002384746,"about_ca_topic_score_gemma":0.00545928,"domain_scores_codex":[0.9967425,0.0009230346,0.0003297046,0.0003842636,0.001063791,0.0005566878],"domain_scores_gemma":[0.9932234,0.0006845418,0.0002528151,0.0002342268,0.003128586,0.002476437],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001458095,0.0002870324,0.0009122048,0.0002437823,0.00002041588,0.001580209,0.0001731977,0.00004825542,0.002066342,0.001760838,0.8930296,0.09973227],"study_design_scores_gemma":[0.00006701807,0.0001121604,0.001947987,0.0006934919,0.00002036602,0.001534801,0.0001500475,0.00005920843,0.0004509951,0.0008901628,0.9940581,0.00001563369],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"empirical","genre_scores_codex":[0.01087548,0.08983749,0.002253091,0.7107055,0.08565712,0.0008658527,0.0006722044,0.0003980847,0.09873508],"genre_scores_gemma":[0.08936264,0.1354873,0.01435546,0.2435983,0.1426449,0.001985036,0.003327372,0.0003116082,0.3689274],"genre_candidate":"empirical","genre_consensus":null,"teacher_disagreement_score":0.01122737,"threshold_uncertainty_score":0.04965478,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1247682909784304,"score_gpt":0.4383878854572825,"score_spread":0.313619594478852,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}