{"id":"W1967542752","doi":"10.1002/mus.10001","title":"Familial amyotrophic lateral sclerosis","year":2002,"lang":"en","type":"review","venue":"Muscle & Nerve","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":229,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal General Hospital","funders":"","keywords":"Amyotrophic lateral sclerosis; Excitotoxicity; SOD1; Neuroscience; Disease; Context (archaeology); Neurofilament; Biology; Genetics; Medicine; Programmed cell death; Immunology; Apoptosis; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","insufficient_payload"],"consensus_categories":["insufficient_payload"],"category_scores_codex":[0.0003602803,0.001010856,0.003388332,0.000520786,0.0002216808,0.0001593342,0.0007056777,0.001023406,0.003743351],"category_scores_gemma":[0.0001340099,0.000750911,0.00180309,0.001029284,0.0002266427,0.0001743537,0.0004701862,0.00188615,0.004172452],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007651139,"about_ca_system_score_gemma":0.0003168674,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000322346,"about_ca_topic_score_gemma":0.000009407425,"domain_scores_codex":[0.9944054,0.0004207322,0.001263182,0.001260848,0.001269352,0.001380437],"domain_scores_gemma":[0.9970575,0.0001447734,0.0003474986,0.001508492,0.0001956277,0.0007461004],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0000221581,0.0002242192,0.00001854926,0.008535029,0.0002899109,0.0004021985,0.00005246718,4.290043e-7,0.00005494486,0.00003480796,0.006992899,0.9833724],"study_design_scores_gemma":[0.001070924,0.000408705,0.003305529,0.01808773,0.001066862,0.0001396399,0.000002996645,0.00004882297,0.000001285796,0.00001582309,0.9751368,0.0007148604],"study_design_candidate":"design_other","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.001753754,0.991778,0.000004129579,0.0002825915,0.0005753275,0.00190374,0.0001251689,0.0003050133,0.003272272],"genre_scores_gemma":[0.001334663,0.9858931,0.0002206339,0.0002025281,0.001931775,0.000358546,0.0003194404,0.0003105726,0.009428787],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.9826576,"threshold_uncertainty_score":0.9994942,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1494161575997246,"score_gpt":0.3455112308361831,"score_spread":0.1960950732364585,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}