{"id":"W1971734644","doi":"10.1016/j.jaci.2008.09.037","title":"Omenn syndrome: Inflammation in leaky severe combined immunodeficiency","year":2008,"lang":"en","type":"review","venue":"Journal of Allergy and Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":251,"is_retracted":false,"has_abstract":false,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Severe combined immunodeficiency; Immunology; Biology; Inflammation; Primary immunodeficiency; Immunodeficiency; Pneumonitis; Failure to thrive; Immune system; Medicine; Gene; Genetics; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002970842,0.001060433,0.001938718,0.002012699,0.0002122434,0.0007340029,0.0009462968,0.001454407,0.001523876],"category_scores_gemma":[0.000649367,0.0002254153,0.0003647164,0.001509201,0.0005085965,0.001181039,0.0006155877,0.001484987,0.001101554],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000335962,"about_ca_system_score_gemma":0.0004866999,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005974193,"about_ca_topic_score_gemma":0.001050698,"domain_scores_codex":[0.9998192,0.00002789072,0.00003888021,0.00003213228,0.00005971456,0.00002226889],"domain_scores_gemma":[0.9997194,0.000118513,0.00006776422,0.000008367298,0.00003871572,0.00004710959],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0002110062,0.00007998915,0.001508627,0.008236753,0.0001409802,0.02074802,0.00007328451,0.0004089299,0.0034786,0.001502146,0.04740921,0.9162026],"study_design_scores_gemma":[0.0001374669,0.000176544,0.007388356,0.004289533,0.0005174619,0.1999425,0.0002107102,0.0003922443,0.00112963,0.002493395,0.7832418,0.00008031228],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0004872647,0.9974601,0.0003219901,0.0004026167,0.0004465803,0.000003501518,0.00001341541,0.00001377533,0.0008508046],"genre_scores_gemma":[0.006210146,0.98989,0.0004359783,0.0006044148,0.00187413,0.00000750802,0.00005725394,0.000003036913,0.0009174033],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.002012699,"threshold_uncertainty_score":0.005097866,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02752060397206042,"score_gpt":0.311880225667907,"score_spread":0.2843596216958466,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}