{"id":"W1972771185","doi":"10.1038/nn884","title":"Early mitochondrial calcium defects in Huntington's disease are a direct effect of polyglutamines","year":2002,"lang":"en","type":"article","venue":"Nature Neuroscience","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":1024,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of British Columbia","funders":"National Institute on Aging","keywords":"Huntingtin; Huntingtin Protein; Neurodegeneration; Mitochondrion; Biology; Huntington's disease; Calcium; Cell biology; Mutant; Genetically modified mouse; Trinucleotide repeat expansion; Transgene; Molecular biology; Genetics; Gene; Pathology; Internal medicine; Medicine; Disease; Allele","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01598198027826318,"score_gpt":0.2652335088383072,"score_spread":0.249251528560044,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}