{"id":"W1973262220","doi":"10.1007/s00467-007-0604-1","title":"Hemolytic uremic syndrome (HUS) secondary to cobalamin C (cblC) disorder","year":2007,"lang":"en","type":"article","venue":"Pediatric Nephrology","topic":"Porphyrin Metabolism and Disorders","field":"Biochemistry, Genetics and Molecular Biology","cited_by":112,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Manitoba; Western University","funders":"","keywords":"Medicine; Cobalamin; Pediatrics; Internal medicine; Diarrhea; Disease; Vitamin B12","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001699941,0.0009845828,0.0007318266,0.0008694835,0.001126998,0.0004498542,0.0003768586,0.001250178,0.002466073],"category_scores_gemma":[0.001227656,0.0003676565,0.0002984961,0.0007371728,0.0008061285,0.0004100253,0.0006105929,0.00103295,0.0003736551],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006209763,"about_ca_system_score_gemma":0.0008481555,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003443917,"about_ca_topic_score_gemma":0.002053244,"domain_scores_codex":[0.9997672,0.00003404457,0.00002431251,0.0000359819,0.00004760976,0.00009086477],"domain_scores_gemma":[0.9992118,0.0002902573,0.0001651695,0.00003715296,0.00004766251,0.0002478786],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0002606562,0.00006292234,0.03038113,0.00009807006,0.0000267826,0.9567258,0.0001228333,0.0001147613,0.006160671,0.0006282476,0.0007913525,0.004626756],"study_design_scores_gemma":[0.00007140588,0.0001250241,0.03320372,0.00001659816,0.0000552134,0.960068,0.00009306468,0.0005027396,0.004225753,0.0003609828,0.001268572,0.000008922939],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9807325,0.002996206,0.001640182,0.0009591779,0.0001088472,0.00005449609,0.0001684665,0.0002105518,0.01312958],"genre_scores_gemma":[0.9979882,0.0005738065,0.0003687147,0.0002184774,0.0001135759,0.000005861698,0.00006240176,0.000008549471,0.0006602696],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003443917,"threshold_uncertainty_score":0.008249879,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003528052274271957,"score_gpt":0.2230967245808547,"score_spread":0.2195686723065828,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}