{"id":"W1977119785","doi":"10.1071/rd02060","title":"Development of infertility at young adult age in a mouse model of human Sandhoff disease","year":2002,"lang":"en","type":"article","venue":"Reproduction Fertility and Development","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":13,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital","funders":"","keywords":"Sandhoff disease; Infertility; Disease; Biology; Medicine; Pathology; Pregnancy; Genetics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000573765,0.0001763465,0.000394463,0.0001960917,0.0001426669,0.000007006503,0.00007739624,0.00007801102,0.0001242714],"category_scores_gemma":[0.0003838783,0.0001647279,0.0000481131,0.0002213419,0.000174384,0.0001036347,0.0001740714,0.000152082,0.000008527248],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000376721,"about_ca_system_score_gemma":0.0001942869,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00006553878,"about_ca_topic_score_gemma":0.0003830413,"domain_scores_codex":[0.9976292,0.0000541655,0.0008377515,0.0006375258,0.0005714453,0.0002699541],"domain_scores_gemma":[0.9988596,0.00001151834,0.0001202283,0.0005257035,0.0002744405,0.0002085474],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.002738358,0.003243286,0.7960153,0.002477121,0.0001114906,0.00001701682,0.03045464,0.0001002635,0.1433561,0.00002896517,0.00005588132,0.02140154],"study_design_scores_gemma":[0.001313186,0.00003843475,0.8740346,0.00008620362,0.00001283287,0.000001963276,0.0003092412,0.0006894146,0.1232459,0.0000452636,0.00007074238,0.0001521929],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9982015,0.0004456936,0.0001467991,0.0001164981,0.00002533586,0.0006005302,0.000004580592,0.00003372252,0.0004253489],"genre_scores_gemma":[0.9941226,0.00003650356,0.003842311,0.00001876029,0.000006810413,0.00005234042,0.00002806715,0.00001324103,0.001879368],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.07801926,"threshold_uncertainty_score":0.671741,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.07219730857773546,"score_gpt":0.2998121427266666,"score_spread":0.2276148341489312,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}