{"id":"W1982161552","doi":"10.1111/j.1365-2990.2005.00694.x","title":"Delayed spinocerebellar ataxia in transgenic mice expressing mutant ubiquitin","year":2005,"lang":"en","type":"article","venue":"Neuropathology and Applied Neurobiology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":13,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Canadian Institutes of Health Research","keywords":"Neurodegeneration; Spinocerebellar ataxia; Biology; Gene isoform; Mutant; Proteolysis; Cell biology; Proteasome; Cerebellum; Ubiquitin; Purkinje cell; Genetically modified mouse; Transgene; Phenotype; Ataxia; Neuroscience; Genetics; Disease; Gene; Biochemistry; Medicine; Internal medicine","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002265942,0.0008540257,0.0003409148,0.0007301877,0.0002826572,0.0004575278,0.0005265973,0.0009074321,0.003585311],"category_scores_gemma":[0.0002137387,0.0004435152,0.0002915604,0.000256703,0.0006374725,0.0004512504,0.0002871655,0.001189552,0.001153797],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006076191,"about_ca_system_score_gemma":0.0002879413,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009294018,"about_ca_topic_score_gemma":0.001516039,"domain_scores_codex":[0.9997897,0.00002956268,0.00002697629,0.00007038302,0.00004535559,0.00003812482],"domain_scores_gemma":[0.9996278,0.00003769341,0.0001605718,0.00003388855,0.00003179045,0.0001082049],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0002912185,0.0001481515,0.0002310018,0.00004472109,0.00001383328,0.0005090134,0.00004208965,0.000087774,0.9960205,0.0006609831,0.0001597463,0.001790924],"study_design_scores_gemma":[0.0007005698,0.002427758,0.01183451,0.00008715194,0.0001702417,0.005438759,0.0001135164,0.004266825,0.9596915,0.001607515,0.01361453,0.00004698975],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9839678,0.001533931,0.007045945,0.0004121666,0.0001587924,0.0001285076,0.001321248,0.0009641831,0.004467307],"genre_scores_gemma":[0.9732105,0.001837897,0.00787271,0.0001586951,0.00005688695,0.0001993222,0.001548453,0.0001808615,0.01493476],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003585311,"threshold_uncertainty_score":0.01199406,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02037982844201777,"score_gpt":0.2494195238406992,"score_spread":0.2290396953986814,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}