{"id":"W1982369903","doi":"10.1002/mus.1067","title":"Severe infantile axonal neuropathy with respiratory failure","year":2001,"lang":"en","type":"article","venue":"Muscle & Nerve","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":34,"is_retracted":false,"has_abstract":true,"ca_institutions":"London Health Sciences Centre; Alberta Children's Hospital","funders":"","keywords":"Medicine; Respiratory failure; Peripheral neuropathy; Pediatrics; Respiratory system; Physical medicine and rehabilitation; Neuroscience; Internal medicine; Psychology; Endocrinology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003388788,0.001654485,0.0006830833,0.0006855819,0.0008965924,0.0004177926,0.0004996886,0.001214779,0.001494509],"category_scores_gemma":[0.001867454,0.0004705556,0.0004674201,0.0003680654,0.0006532709,0.0003773523,0.0009516611,0.001137017,0.0003144065],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004855562,"about_ca_system_score_gemma":0.0002692175,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00138865,"about_ca_topic_score_gemma":0.002283949,"domain_scores_codex":[0.9995238,0.00007477916,0.00004307104,0.00009037938,0.00008285946,0.0001852131],"domain_scores_gemma":[0.9993351,0.0001332157,0.0002185093,0.00005577732,0.00004107501,0.0002162856],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001418211,0.000102192,0.07660838,0.00008350379,0.00004853428,0.9088438,0.0005767655,0.0003534851,0.003273229,0.0003524545,0.0006195993,0.008996338],"study_design_scores_gemma":[0.00001730132,0.0006474161,0.06603911,0.00001582799,0.00003073438,0.9311629,0.0001508304,0.0003036935,0.0008368676,0.0001153621,0.0006631795,0.00001677938],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9948549,0.00074061,0.001080195,0.0001783449,0.00003811768,0.00003712328,0.00005934275,0.00007520846,0.002936094],"genre_scores_gemma":[0.9983321,0.0002699633,0.0004602468,0.0001708296,0.00005659083,0.0000136724,0.00004778774,0.000009697083,0.0006391247],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001654485,"threshold_uncertainty_score":0.004999578,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02874125912896945,"score_gpt":0.2347549660476051,"score_spread":0.2060137069186357,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}