{"id":"W1985395003","doi":"10.1007/s10875-013-9952-8","title":"Severe Combined Immunodeficiency (SCID) in Canadian Children: A National Surveillance Study","year":2013,"lang":"en","type":"article","venue":"Journal of Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":33,"is_retracted":false,"has_abstract":false,"ca_institutions":"Centre Hospitalier Universitaire Sainte-Justine; University of Manitoba; Health Canada; BC Children's Hospital; Dalhousie University; Canadian Nutrition Society; University of British Columbia; University of Alberta; Université de Montréal; Child and Family Research Institute","funders":"Health Canada","keywords":"Medicine; Pediatrics; Incidence (geometry); Severe combined immunodeficiency; Newborn screening; Population; Hematopoietic stem cell transplantation; Transplantation; Cumulative incidence; Primary immunodeficiency; Surgery; Internal medicine; Disease; Environmental health","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","insufficient_payload"],"consensus_categories":["insufficient_payload"],"category_scores_codex":[0.003874514,0.0003047324,0.001139806,0.0006683549,0.0002463075,0.00004333877,0.001101754,0.0005448103,0.001447133],"category_scores_gemma":[0.002162311,0.000257317,0.0003760824,0.0005588295,0.0005657416,0.0003777457,0.0001315437,0.001811923,0.0009300448],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001599591,"about_ca_system_score_gemma":0.001454782,"about_ca_topic_candidate":true,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.05978636,"about_ca_topic_score_gemma":0.007262172,"domain_scores_codex":[0.9944962,0.001311312,0.002788415,0.0003610775,0.0001383972,0.00090464],"domain_scores_gemma":[0.9970484,0.0007441944,0.001018834,0.0004040251,0.0007451415,0.00003938018],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0006705744,0.004006953,0.9566008,0.000004684964,0.001071515,0.00003123242,0.0007859746,0.0001108204,0.004545897,0.0006811377,0.001334766,0.03015568],"study_design_scores_gemma":[0.007800587,0.001861639,0.9831775,0.00002835567,0.00002429247,0.0003623761,0.0009372963,0.0000105959,0.00004666859,0.0006683638,0.004782255,0.0003000581],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9767375,0.01664077,0.000006335535,0.001105949,0.002738802,0.0005434619,0.00001123686,0.0000212869,0.002194645],"genre_scores_gemma":[0.9986301,0.0003630554,0.00001830333,0.0004362044,0.00001998904,0.00001795231,0.00002437978,0.00002312989,0.0004668852],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05252419,"threshold_uncertainty_score":0.9999879,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01881375564755083,"score_gpt":0.3080998695896594,"score_spread":0.2892861139421086,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}