{"id":"W1988447677","doi":"10.1002/ana.23582","title":"Glucose metabolism and pancreatic defects in spinal muscular atrophy","year":2012,"lang":"en","type":"article","venue":"Annals of Neurology","topic":"Neurogenetic and Muscular Disorders Research","field":"Medicine","cited_by":183,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario; Ottawa Hospital; University of Ottawa","funders":"Eunice Kennedy Shriver National Institute of Child Health and Human Development; Canadian Institutes of Health Research","keywords":"SMA*; Spinal muscular atrophy; SMN1; Endocrinology; Internal medicine; Hyperglucagonemia; Carbohydrate metabolism; Insulin; Motor neuron; Biology; Glucagon; Medicine; Disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001379565,0.0003651261,0.0001169912,0.0005226449,0.0001229758,0.0001807656,0.0001162316,0.0002378962,0.001240854],"category_scores_gemma":[0.0001356215,0.00008807435,0.00009994347,0.0002242729,0.0003022204,0.0001492716,0.0001794713,0.0002352695,0.0001282038],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001846815,"about_ca_system_score_gemma":0.00009627467,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002729266,"about_ca_topic_score_gemma":0.0004970471,"domain_scores_codex":[0.9999536,0.00001328911,0.00000527623,0.000009823053,0.00001111571,0.000006905063],"domain_scores_gemma":[0.9999157,0.00001402866,0.0000411885,0.000003735326,0.000006535689,0.00001876937],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.004911119,0.0004183547,0.3188305,0.0004945791,0.0001651206,0.01539357,0.0002801156,0.0006412527,0.6164925,0.001275114,0.000742271,0.04035538],"study_design_scores_gemma":[0.0001157586,0.002224656,0.9037992,0.0001078603,0.000212796,0.02927524,0.0002815214,0.001019783,0.05865743,0.0008554354,0.003435152,0.00001515337],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9943322,0.004266474,0.0002526895,0.00008806311,0.000008352661,0.000005876316,0.00006718408,0.00001230588,0.0009668946],"genre_scores_gemma":[0.9966986,0.002455594,0.0003245923,0.00003311947,0.00001343182,0.000007698512,0.00009785956,0.00000287181,0.0003661461],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001240854,"threshold_uncertainty_score":0.004151046,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.05118377043053499,"score_gpt":0.3464961443683453,"score_spread":0.2953123739378103,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}