{"id":"W1991763259","doi":"10.1097/mph.0b013e31806451d3","title":"Hyperimmunoglobulinemia in Pediatric-onset Type 1 Gaucher Disease and Effects of Enzyme Replacement Therapy","year":2007,"lang":"en","type":"article","venue":"Journal of Pediatric Hematology/Oncology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":28,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; University of Toronto","funders":"","keywords":"Medicine; Enzyme replacement therapy; Disease; Immunology; Glucocerebrosidase; Gaucher's disease; Immunoglobulin G; Antibody; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001890441,0.0002240469,0.001025041,0.0008782241,0.00003952472,0.000005996145,0.0002081249,0.0003659741,0.0001125565],"category_scores_gemma":[0.001980324,0.0001782624,0.000150922,0.0008069039,0.0001440379,0.00009010243,0.00009811544,0.0007598719,0.00001072107],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003107053,"about_ca_system_score_gemma":0.001430351,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0000236353,"about_ca_topic_score_gemma":0.00001111545,"domain_scores_codex":[0.9972191,0.0003014164,0.001203575,0.0002615039,0.000490263,0.0005241486],"domain_scores_gemma":[0.996769,0.001354367,0.0006903727,0.0002673254,0.0004718982,0.000447103],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.01142712,0.001707575,0.9691466,0.0006784978,0.0001277678,0.00542233,0.0005826044,0.000002649502,0.001332321,0.00004611608,0.006692758,0.002833657],"study_design_scores_gemma":[0.02923484,0.01426979,0.936738,0.00008299709,0.0008843097,0.004611331,0.0006073019,0.00003649354,0.00377235,0.0003981412,0.008928522,0.0004359512],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9428105,0.05474481,0.00009565111,0.001030828,0.0004615952,0.0005166021,0.000001652562,0.00001058531,0.0003277631],"genre_scores_gemma":[0.9768167,0.02100962,0.001112852,0.0003485394,0.0005981633,0.000007405234,0.000003448192,0.00002815195,0.00007516236],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.03400614,"threshold_uncertainty_score":0.7269329,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02131855022064206,"score_gpt":0.3471910684207781,"score_spread":0.325872518200136,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}