{"id":"W2002368498","doi":"10.1111/jnc.12493","title":"Mutant <scp>SOD</scp>1 inhibits <scp>ER</scp>‐Golgi transport in amyotrophic lateral sclerosis","year":2013,"lang":"en","type":"article","venue":"Journal of Neurochemistry","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":70,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"National Medical Research Council; National Health and Medical Research Council; State Government of Victoria; University of Toronto; Victorian Brain Bank; National Science Council; Medical Research Council; Australian Rotary Health; Motor Neurone Disease Research Institute of Australia","keywords":"Golgi apparatus; Endoplasmic reticulum; Cell biology; Unfolded protein response; SOD1; Transport protein; COPII; Biology; Fragmentation (computing); Chemistry; Secretory pathway; Superoxide dismutase; Biochemistry; Oxidative stress","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.000489442,0.0005211178,0.001045192,0.0003614065,0.0001069325,0.0001125298,0.0006271979,0.0003940066,0.0002299709],"category_scores_gemma":[0.001042485,0.0004271537,0.0004847886,0.0007700044,0.0002370561,0.0005443407,0.0001240843,0.002274081,0.0001361597],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003159632,"about_ca_system_score_gemma":0.0003685202,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00006849262,"about_ca_topic_score_gemma":0.000003023527,"domain_scores_codex":[0.9950252,0.0001155906,0.001554811,0.000570004,0.001584835,0.00114956],"domain_scores_gemma":[0.9967771,0.0003484532,0.0006119248,0.0005651339,0.0006827952,0.001014603],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0000426002,0.0004449296,0.04580643,0.0002408555,0.00009504381,0.001218275,0.0003533285,0.00004748595,0.9452708,0.000001774875,0.005897161,0.0005812898],"study_design_scores_gemma":[0.003880003,0.0005489894,0.8497892,0.0009763588,0.00009547315,0.001899541,0.0001689447,0.0002429064,0.1393135,0.0001050412,0.002875718,0.0001043388],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9952478,0.0004557516,0.00001587706,0.001987841,0.0002293586,0.0004158238,0.00001335004,0.00005270668,0.001581524],"genre_scores_gemma":[0.9947901,0.0009327159,0.0002967551,0.001381098,0.0006034619,0.00002714484,0.00001405274,0.0001081628,0.001846491],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.8059573,"threshold_uncertainty_score":0.999818,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02470575319104587,"score_gpt":0.2531764832344719,"score_spread":0.2284707300434261,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}