{"id":"W2003228110","doi":"10.1007/s00415-010-5726-x","title":"Heterozygous X-linked adrenoleukodystrophy-associated myelopathy mimicking primary progressive multiple sclerosis","year":2010,"lang":"en","type":"letter","venue":"Journal of Neurology","topic":"Peroxisome Proliferator-Activated Receptors","field":"Biochemistry, Genetics and Molecular Biology","cited_by":16,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"Università degli Studi di Siena; Ryerson University","keywords":"Adrenoleukodystrophy; Neuroradiology; Medicine; Myelopathy; Neurology; Multiple sclerosis; Leukodystrophy; Pathology; Internal medicine; Spinal cord; Immunology; Disease","routes":{"ca_aff":false,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","research_integrity"],"consensus_categories":["research_integrity"],"category_scores_codex":[0.0003154071,0.0006706761,0.001065276,0.0003840822,0.0001548974,0.00007850848,0.001001184,0.004810812,0.00004494929],"category_scores_gemma":[0.0006472804,0.0006087833,0.000610694,0.000173808,0.0003184426,0.00001681971,0.0003226415,0.008020502,0.00001315557],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00007602809,"about_ca_system_score_gemma":0.0004692373,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000005251492,"about_ca_topic_score_gemma":0.000005565064,"domain_scores_codex":[0.996188,0.0006290704,0.00109791,0.000705397,0.0005281878,0.0008514328],"domain_scores_gemma":[0.9960988,0.0001208899,0.002358529,0.0005742795,0.000666499,0.0001809995],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0005987335,0.000156866,0.002427244,0.00005109518,0.0004870819,0.001401849,0.00003340319,0.00002125789,0.8166294,6.035746e-8,0.1769828,0.001210142],"study_design_scores_gemma":[0.005333074,0.007553773,0.006792128,0.0002419703,0.0004177986,0.005891425,0.000008106916,0.00002776783,0.2546307,0.00003102965,0.7176461,0.001426088],"study_design_candidate":"bench_or_experimental","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9438293,0.001109023,0.00004029027,0.05135423,0.003159589,0.0003411737,0.00008329738,0.00002978028,0.00005329732],"genre_scores_gemma":[0.6427295,0.0005542761,0.000569553,0.3446684,0.0104515,0.00004075625,0.0005483767,0.0002885463,0.0001490977],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.5619987,"threshold_uncertainty_score":0.9996364,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01781133629892706,"score_gpt":0.2147832259787623,"score_spread":0.1969718896798353,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}