{"id":"W2011441484","doi":"10.1159/000091609","title":"Pulmonary Fibrosis in Hermansky-Pudlak Syndrome","year":2006,"lang":"en","type":"review","venue":"Respiration","topic":"melanin and skin pigmentation","field":"Biochemistry, Genetics and Molecular Biology","cited_by":85,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia; Vancouver General Hospital; University of Manitoba","funders":"","keywords":"Hermansky–Pudlak syndrome; Medicine; Pulmonary fibrosis; Oculocutaneous albinism; Cystic fibrosis; Bleeding diathesis; Pathology; Lung; Lipofuscin; Fibrosis; Cystinosis; Albinism; Immunology; Internal medicine; Genetics; Platelet; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002459853,0.0007508848,0.001147105,0.0017941,0.0002594517,0.0004812819,0.0005076673,0.0009940715,0.002077013],"category_scores_gemma":[0.0004327321,0.000149967,0.000242617,0.001534301,0.0003488506,0.000734054,0.0003301112,0.0007104933,0.001675335],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003439008,"about_ca_system_score_gemma":0.0005245351,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008379008,"about_ca_topic_score_gemma":0.001414955,"domain_scores_codex":[0.9998913,0.00001956964,0.00001805681,0.00002152347,0.00003715218,0.00001243852],"domain_scores_gemma":[0.9998802,0.00004905797,0.0000254564,0.000004395383,0.00002388381,0.00001699484],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00007901029,0.00005965927,0.0009099022,0.006342199,0.00005806263,0.006632371,0.0000897798,0.0002890645,0.002461519,0.001077798,0.02104619,0.9609545],"study_design_scores_gemma":[0.00006344481,0.0001859843,0.009985959,0.003408494,0.000220813,0.1380828,0.0002358677,0.0002307328,0.00156424,0.002610025,0.8433674,0.00004424117],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.001043748,0.9956934,0.0003564766,0.0003085186,0.0001957566,0.000007029049,0.00001736663,0.00002498782,0.002352718],"genre_scores_gemma":[0.00723635,0.9899899,0.0004212902,0.0002637818,0.000309133,0.000009249723,0.00004504038,0.000003323679,0.001722044],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.002077013,"threshold_uncertainty_score":0.006948292,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0282765337409138,"score_gpt":0.3169288454183876,"score_spread":0.2886523116774737,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}