{"id":"W2011441484","doi":"10.1159/000091609","title":"Pulmonary Fibrosis in Hermansky-Pudlak Syndrome","year":2006,"lang":"en","type":"review","venue":"Respiration","topic":"melanin and skin pigmentation","field":"Biochemistry, Genetics and Molecular Biology","cited_by":85,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia; Vancouver General Hospital; University of Manitoba","funders":"","keywords":"Hermansky–Pudlak syndrome; Medicine; Pulmonary fibrosis; Oculocutaneous albinism; Cystic fibrosis; Bleeding diathesis; Pathology; Lung; Lipofuscin; Fibrosis; Cystinosis; Albinism; Immunology; Internal medicine; Genetics; Platelet; Biology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001684522,0.0002148802,0.0003896013,0.0001209726,0.00003461476,0.00002862654,0.000127779,0.0003787805,0.00002191125],"category_scores_gemma":[0.00001800104,0.0002029233,0.0001606824,0.0001539472,0.00001678283,0.00000467068,0.00003951009,0.0001047796,0.00005863063],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00005105941,"about_ca_system_score_gemma":0.00008624561,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00003132009,"about_ca_topic_score_gemma":0.00003276518,"domain_scores_codex":[0.9987618,0.0001620016,0.0004260798,0.0003620186,0.0001272716,0.0001608311],"domain_scores_gemma":[0.9994892,0.00001069592,0.0001721567,0.0002785912,0.00001929135,0.00003000037],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0000138529,0.00009476388,0.00008981661,0.00397555,0.00003580134,0.00007717924,0.000006484602,0.0000296874,0.002493758,0.00004905154,0.001922798,0.9912112],"study_design_scores_gemma":[0.0001008522,0.00009025115,0.0001445047,0.0009898235,0.00004970046,0.0001023157,0.000001468604,0.00001108923,0.0001844826,0.0000132307,0.9980839,0.0002284178],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.001513269,0.9943902,0.0001320535,0.000005720432,0.0001437462,0.0004643347,0.00002758133,0.00001058007,0.00331246],"genre_scores_gemma":[0.001045952,0.9928316,0.00009605414,0.00003225969,0.0002611916,0.0001312458,0.003909485,0.00003808371,0.00165415],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.996161,"threshold_uncertainty_score":0.8274972,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0282765337409138,"score_gpt":0.3169288454183876,"score_spread":0.2886523116774737,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}