{"id":"W2016457825","doi":"10.1016/j.cjca.2014.07.341","title":"PLASMA BIOMARKER ANALYSIS IN PATIENTS WITH CARDIOMYOPATHY SECONDARY TO FABRY DISEASE : INSIGHT INTO THE PATHOPHYSIOLOGY OF FABRY CARDIOMYOPATHY","year":2014,"lang":"en","type":"article","venue":"Canadian Journal of Cardiology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Alberta Hospital Edmonton","funders":"","keywords":"Medicine; Fabry disease; Globotriaosylceramide; Enzyme replacement therapy; Cardiomyopathy; Pathophysiology; Internal medicine; Natriuretic peptide; Heart failure; Biomarker; Cardiology; Alpha-galactosidase; Left ventricular hypertrophy; Atrial natriuretic peptide; Brain natriuretic peptide; Sphingolipid; Endocrinology; Disease; Blood pressure","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005709164,0.0006293926,0.0009639072,0.000941277,0.0005143061,0.0009931921,0.0003162101,0.001116942,0.0007577282],"category_scores_gemma":[0.002121647,0.0002285795,0.000391671,0.0008120783,0.0003968573,0.000476284,0.0002478673,0.0006128518,0.000189704],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000391323,"about_ca_system_score_gemma":0.0004796123,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001266352,"about_ca_topic_score_gemma":0.001334223,"domain_scores_codex":[0.9996728,0.00007325187,0.00005471473,0.00006172363,0.00008164694,0.00005591229],"domain_scores_gemma":[0.9993805,0.0002568277,0.0001601692,0.00002683249,0.0000705636,0.0001051417],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001703358,0.0001156682,0.951871,0.0001032143,0.000164704,0.0123145,0.0003486132,0.0003567983,0.0157091,0.0002439933,0.0006101692,0.016459],"study_design_scores_gemma":[0.00006104728,0.0006889703,0.9710497,0.00007093531,0.0002361552,0.02090228,0.0005322607,0.001941507,0.002825269,0.0007061144,0.000956933,0.00002878932],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9929405,0.004413451,0.0005921862,0.0004108028,0.00004774623,0.00001448811,0.0001485756,0.00002961602,0.001402704],"genre_scores_gemma":[0.998669,0.0005915656,0.0003183384,0.0001742435,0.00005897009,0.000004847655,0.0000767981,0.000003554737,0.0001027041],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001266352,"threshold_uncertainty_score":0.003019392,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.00748754112442473,"score_gpt":0.227566411112456,"score_spread":0.2200788699880312,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}