{"id":"W2018994479","doi":"10.1093/brain/123.7.1505","title":"Preserved slow conducting corticomotoneuronal projections in amyotrophic lateral sclerosis with autosomal recessive D90A CuZn-superoxide dismutase mutation","year":2000,"lang":"en","type":"article","venue":"Brain","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":52,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"","keywords":"Amyotrophic lateral sclerosis; Superoxide dismutase; SOD1; Medicine; Mutation; Dismutase; Internal medicine; Pathology; Genetics; Endocrinology; Biology; Gene; Disease; Oxidative stress","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["insufficient_payload"],"consensus_categories":[],"category_scores_codex":[0.0002977701,0.0002947183,0.0004170939,0.0002534873,0.0002175128,0.00009830226,0.0001785168,0.0001364347,0.001385894],"category_scores_gemma":[0.0002934981,0.0002349448,0.00009468093,0.0008176974,0.0002496002,0.0005151221,0.00006100639,0.000690796,0.0001085977],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002492318,"about_ca_system_score_gemma":0.0002645644,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001142874,"about_ca_topic_score_gemma":0.0002336159,"domain_scores_codex":[0.9970509,0.0003324793,0.0005302317,0.0006543233,0.0007165183,0.0007155831],"domain_scores_gemma":[0.9988934,0.0001781985,0.00009878275,0.0004070311,0.0001427048,0.0002799292],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.005777252,0.002083382,0.2231395,0.0003047468,0.0003404059,0.002559613,0.003481366,0.002928865,0.708557,0.0001286133,0.004322665,0.04637663],"study_design_scores_gemma":[0.005785393,0.001196566,0.9745246,0.0005823898,0.00004889386,0.0004270565,0.0001400048,0.01240838,0.003717235,0.00007455041,0.0007202784,0.0003746081],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9831355,0.00003988012,0.00002578331,0.01461183,0.00005762654,0.001269327,0.00003054589,0.0001651252,0.0006644212],"genre_scores_gemma":[0.9935884,0.00003492041,0.001195318,0.001132289,0.0001354469,0.000272958,0.0001351586,0.00007142825,0.00343401],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.7513852,"threshold_uncertainty_score":0.999527,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06296837968081538,"score_gpt":0.3010999802199972,"score_spread":0.2381316005391819,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}