{"id":"W2022233059","doi":"10.1684/epd.2016.0844","title":"Neuronal ceroid lipofuscinoses","year":2016,"lang":"en","type":"review","venue":"Epileptic Disorders","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":147,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Toronto","funders":"","keywords":"Neuroscience; Neuronal ceroid lipofuscinosis; Epilepsy; Atrophy; Pathophysiology; Psychology; Progressive myoclonus epilepsy; Medicine; Pathology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003614951,0.0008102954,0.001173507,0.003630237,0.0003105845,0.0008967817,0.0005932096,0.0008160601,0.003025869],"category_scores_gemma":[0.000660914,0.0001997611,0.0004215968,0.00270932,0.0003484074,0.001175098,0.0007071701,0.001105555,0.00256685],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004883112,"about_ca_system_score_gemma":0.001007461,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009084914,"about_ca_topic_score_gemma":0.001478945,"domain_scores_codex":[0.9998203,0.00002068433,0.00004241583,0.00002685767,0.00007021616,0.00001950212],"domain_scores_gemma":[0.9998042,0.00006448697,0.00004288632,0.000007079426,0.0000556944,0.00002572628],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00004940509,0.00004258859,0.0002962296,0.0156304,0.00008260487,0.0008734529,0.00008933062,0.000185089,0.002179611,0.002442649,0.03598291,0.9421457],"study_design_scores_gemma":[0.00001165922,0.00004290825,0.001078822,0.004001149,0.00008958127,0.008804128,0.00008462156,0.00003817977,0.0005204104,0.001545825,0.9837661,0.00001658917],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001611043,0.998086,0.00009452137,0.0002238231,0.0001427924,0.000005402278,0.00002631167,0.00001178781,0.001248438],"genre_scores_gemma":[0.0007854499,0.9981193,0.0001683466,0.0001323286,0.0001147762,0.000004949086,0.00004466454,0.000001430848,0.0006287339],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.003630237,"threshold_uncertainty_score":0.01012254,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04356249462049851,"score_gpt":0.3597665885275413,"score_spread":0.3162040939070428,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}