{"id":"W2022514980","doi":"10.1093/brain/124.3.522","title":"Oculopharyngeal muscular dystrophy","year":2001,"lang":"en","type":"article","venue":"Brain","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":94,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Oculopharyngeal muscular dystrophy; Muscular dystrophy; Medicine; Physical medicine and rehabilitation; Internal medicine","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00004784775,0.0001187731,0.0001002357,0.0000552233,0.0001055525,0.00004144832,0.0002244857,0.00002392508,0.0003763311],"category_scores_gemma":[0.0005059422,0.000111173,0.00007458395,0.000244805,0.00005836031,0.00007149823,0.00005855415,0.00004843773,0.0005160644],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0000122357,"about_ca_system_score_gemma":0.00002909256,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000005184602,"about_ca_topic_score_gemma":0.000002025577,"domain_scores_codex":[0.9988395,0.0001627924,0.0001153995,0.000386627,0.0002393646,0.000256341],"domain_scores_gemma":[0.9994364,0.000103434,0.00003034857,0.0002865488,0.00001726603,0.0001259617],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.00001491132,0.00006007505,0.0006086917,0.000003264351,0.000001298323,0.0001810928,0.00003336051,0.0000812795,0.9912328,0.001077309,0.004387894,0.002318011],"study_design_scores_gemma":[0.0004864616,0.00008340645,0.01507342,0.000004031323,0.000006111929,0.00004859755,0.00001149964,0.0002448434,0.9196975,0.0005961873,0.06356199,0.0001858954],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9911498,0.00004174247,0.0004085038,0.001728935,0.0001941421,0.0001613633,0.00001132207,0.00009432868,0.006209906],"genre_scores_gemma":[0.9924173,0.00001569621,0.0001555703,0.005059071,0.0001427073,0.00002115777,0.000001707072,0.00002010802,0.002166709],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.07153526,"threshold_uncertainty_score":0.6633136,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02690057022934074,"score_gpt":0.2678565420343755,"score_spread":0.2409559718050347,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}