{"id":"W2025620576","doi":"10.1177/08830738050200022101","title":"Type I Spinal Muscular Atrophy Can Mimic Sensory-Motor Axonal Neuropathy","year":2005,"lang":"en","type":"article","venue":"Journal of Child Neurology","topic":"Neurogenetic and Muscular Disorders Research","field":"Medicine","cited_by":31,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Montreal Children's Hospital","funders":"","keywords":"Spinal muscular atrophy; Medicine; Atrophy; Electromyography; Hereditary motor and sensory neuropathy; Pathology; Muscle atrophy; Anatomy; Neuroscience; Physical medicine and rehabilitation; Psychology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002265845,0.001539441,0.0006329981,0.0007336239,0.0004911974,0.0004780999,0.0005703064,0.001488785,0.001783283],"category_scores_gemma":[0.002424206,0.0003425009,0.0003713276,0.0005849021,0.000749515,0.0006527192,0.0006521803,0.0008259247,0.0007738715],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003883453,"about_ca_system_score_gemma":0.0002423532,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001518392,"about_ca_topic_score_gemma":0.001672917,"domain_scores_codex":[0.9995953,0.00006992235,0.00004599473,0.0000788506,0.00007253279,0.0001372951],"domain_scores_gemma":[0.999352,0.0002031944,0.0002382469,0.00003983162,0.0000395068,0.000127101],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0002985823,0.00007157479,0.1093397,0.0004207394,0.00005976369,0.8460068,0.001012627,0.0005475017,0.0249727,0.001222997,0.002077323,0.01396978],"study_design_scores_gemma":[0.00001966323,0.000281081,0.03981334,0.00005266945,0.00004756328,0.9545231,0.0002563881,0.000284585,0.002718298,0.0004854582,0.001503981,0.00001381635],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9736623,0.004889703,0.002771065,0.000421494,0.0001215933,0.0001176164,0.0001855962,0.0003667144,0.01746389],"genre_scores_gemma":[0.9959395,0.001723442,0.0009289025,0.0002949045,0.00009779885,0.00002043358,0.00009099925,0.00002678005,0.0008772657],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001783283,"threshold_uncertainty_score":0.00596565,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01486158641988312,"score_gpt":0.2803487270772508,"score_spread":0.2654871406573677,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}