{"id":"W2049696934","doi":"10.1007/s10875-012-9778-9","title":"Granulomatous Disease in CVID: Retrospective Analysis of Clinical Characteristics and Treatment Efficacy in a Cohort of 59 Patients","year":2012,"lang":"en","type":"review","venue":"Journal of Clinical Immunology","topic":"Immunodeficiency and Autoimmune Disorders","field":"Immunology and Microbiology","cited_by":141,"is_retracted":false,"has_abstract":false,"ca_institutions":"Centre hospitalier universitaire de Québec; Université Laval","funders":"","keywords":"Medicine; Common variable immunodeficiency; Azathioprine; Hydroxychloroquine; Rituximab; Sulfasalazine; Hypogammaglobulinemia; Internal medicine; Cohort; Infliximab; Thalidomide; Surgery; Gastroenterology; Disease; Immunology; Lymphoma; Ulcerative colitis; Multiple myeloma","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004642752,0.000371102,0.001603383,0.001036571,0.0002335421,0.0006405551,0.0004741575,0.0004486542,0.0004998192],"category_scores_gemma":[0.0009352468,0.0001862263,0.0004987816,0.001426178,0.0002827014,0.0005135085,0.0002631031,0.0003965147,0.0001143804],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000187609,"about_ca_system_score_gemma":0.0005078191,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0005760199,"about_ca_topic_score_gemma":0.0008421912,"domain_scores_codex":[0.9996281,0.00006045359,0.00008304057,0.0001040937,0.00008324546,0.00004105396],"domain_scores_gemma":[0.9993992,0.0002642595,0.0002003442,0.00001988519,0.00005874637,0.000057567],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001019667,0.0002545079,0.7563937,0.003280314,0.0009454761,0.005158082,0.0002098102,0.0001925185,0.001432401,0.0001629368,0.001913738,0.2290368],"study_design_scores_gemma":[0.0001060331,0.0004964239,0.9555559,0.001678547,0.001305666,0.03103114,0.0004618525,0.0001771685,0.0002798943,0.000214773,0.008650569,0.00004219277],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.2813431,0.7168022,0.0003194895,0.0001472871,0.00008855503,0.00003601015,0.0002938272,0.000007951966,0.0009616803],"genre_scores_gemma":[0.5704207,0.4265016,0.0008135635,0.000279307,0.0003867168,0.00005876101,0.001243106,0.00000567723,0.0002905893],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.001603383,"threshold_uncertainty_score":0.002455354,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.06236711853952222,"score_gpt":0.4035070473751677,"score_spread":0.3411399288356455,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}