{"id":"W2057468082","doi":"10.1177/0883073811423973","title":"Alpers Syndrome","year":2011,"lang":"en","type":"article","venue":"Journal of Child Neurology","topic":"Diet and metabolism studies","field":"Medicine","cited_by":18,"is_retracted":false,"has_abstract":true,"ca_institutions":"Calgary Laboratory Services; Alberta Children's Hospital; University of Calgary","funders":"","keywords":"Neuroimaging; Mitochondrial disease; Leigh disease; Pathological; Gold standard (test); Medicine; Disease; Pathology; Encephalopathy; Epilepsy; Bioinformatics; Mutation; Biology; Radiology; Genetics; Internal medicine; Gene; Mitochondrial DNA; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002099217,0.002034985,0.0008286203,0.0009708733,0.0009781916,0.0006856567,0.0005920996,0.001891232,0.01400946],"category_scores_gemma":[0.001567807,0.0001855177,0.0005144341,0.0007932074,0.0006956662,0.0007644307,0.0006081991,0.0008736923,0.002780605],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003985876,"about_ca_system_score_gemma":0.0004567319,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001573047,"about_ca_topic_score_gemma":0.001356016,"domain_scores_codex":[0.999535,0.00006114983,0.00004494201,0.0001397116,0.0001165778,0.0001027564],"domain_scores_gemma":[0.9995517,0.000132615,0.000132999,0.00002372911,0.00007497276,0.00008400484],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0005407846,0.0001006712,0.03027154,0.000758087,0.0002101437,0.8516168,0.0008158466,0.0004714136,0.0196474,0.008578291,0.0150215,0.0719675],"study_design_scores_gemma":[0.00007828865,0.0001584759,0.01773348,0.0002892,0.0001083565,0.9321885,0.000297194,0.0003393007,0.003253354,0.00377602,0.04173936,0.00003841084],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.6929628,0.05792252,0.01244409,0.01232166,0.001974706,0.0004081833,0.003248718,0.001907628,0.2168097],"genre_scores_gemma":[0.9305112,0.009919399,0.003784272,0.003355989,0.0006725267,0.0001036018,0.001244238,0.0001378113,0.05027087],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01400946,"threshold_uncertainty_score":0.04686624,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02237884552428824,"score_gpt":0.2418156737279265,"score_spread":0.2194368282036383,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}