{"id":"W2059470375","doi":"10.4102/sajr.v13i3.500","title":"Infantile Sandhoff's disease","year":2009,"lang":"en","type":"article","venue":"South African Journal of Radiology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":3,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Saskatchewan","funders":"","keywords":"Medicine; Sandhoff disease; Disease; Radiological weapon; Pediatrics; Pathology; Dermatology; Radiology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003232226,0.0001164008,0.0004345892,0.0002857936,0.00005140984,0.00001054585,0.000190571,0.00006538653,0.0003275804],"category_scores_gemma":[0.0007051018,0.00008541426,0.0002061378,0.0002615025,0.0001588835,0.0000633545,0.00001744022,0.0003947033,0.00003567611],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00006790432,"about_ca_system_score_gemma":0.0003605496,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000001490467,"about_ca_topic_score_gemma":2.137197e-7,"domain_scores_codex":[0.9987311,0.0001141816,0.0003642485,0.0001359601,0.0003077811,0.0003467015],"domain_scores_gemma":[0.998732,0.00005811111,0.0002038178,0.0002072755,0.0002208179,0.0005780205],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.01753018,0.001198969,0.8283678,0.0001224689,0.0006355866,0.01484605,0.01075475,0.0002141666,0.009769423,0.001779318,0.06679106,0.04799018],"study_design_scores_gemma":[0.008095617,0.00661345,0.9394286,0.0001220309,0.0003348217,0.007201397,0.002380783,0.0001494882,0.0002153736,0.003213624,0.03189133,0.0003535117],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9863284,0.002518486,0.0004560345,0.006002606,0.000163966,0.0001424435,0.000007285103,0.00001748411,0.004363294],"genre_scores_gemma":[0.9980144,0.00005686843,0.0004721989,0.0007219986,0.0004074666,9.829728e-7,0.000002872505,0.00001111673,0.0003120929],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1110607,"threshold_uncertainty_score":0.3586775,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01512221361768924,"score_gpt":0.2856691237165445,"score_spread":0.2705469100988552,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}