{"id":"W2061060689","doi":"10.1542/peds.111.5.1072","title":"Autosomal Recessive Polycystic Kidney Disease: The Clinical Experience in North America","year":2003,"lang":"en","type":"article","venue":"PEDIATRICS","topic":"Genetic and Kidney Cyst Diseases","field":"Biochemistry, Genetics and Molecular Biology","cited_by":424,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"PKD Australia; University of Alabama at Birmingham; American Society of Nephrology","keywords":"Medicine; Autosomal Recessive Polycystic Kidney Disease; Cohort; Pediatrics; Sibling; Cohort study; Polycystic kidney disease; Internal medicine; Disease","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0009600656,0.0002025456,0.0002681405,0.0006694777,0.0009029506,0.0007909716,0.0003860128,0.0003717113,0.001325609],"category_scores_gemma":[0.00204961,0.0001981829,0.0001402341,0.002034658,0.0006091218,0.0007448203,0.0008225568,0.0003355772,0.0002496221],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00115852,"about_ca_system_score_gemma":0.002445433,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.05846206,"about_ca_topic_score_gemma":0.1075207,"domain_scores_codex":[0.9991739,0.0002692413,0.0001044618,0.0001867236,0.0001493181,0.0001162081],"domain_scores_gemma":[0.9981595,0.0003679649,0.0005193083,0.0001040983,0.0003719242,0.0004772702],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00004051348,0.00006473819,0.9808356,0.00005020406,0.00002492383,0.001663879,0.001759412,0.00004699901,0.0003458528,0.0001098393,0.001309534,0.01374853],"study_design_scores_gemma":[0.00001275254,0.00008256213,0.985324,0.0001085966,0.00002488836,0.005547473,0.004386973,0.0001241356,0.00008765548,0.00008329828,0.004206867,0.00001074624],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9922199,0.003403998,0.0002206117,0.0008470131,0.00002308662,0.00002848597,0.0005495257,0.00001209044,0.002695332],"genre_scores_gemma":[0.9938386,0.003923836,0.0004694921,0.0005734924,0.0000467938,0.00003782885,0.0006283097,0.000008004713,0.0004736419],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05846206,"threshold_uncertainty_score":0.1162435,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01632194950628005,"score_gpt":0.2962295937549733,"score_spread":0.2799076442486933,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}