{"id":"W2062499657","doi":"10.1155/2013/874197","title":"Undiagnosed Chronic Granulomatous Disease,<i>Burkholderia cepacia complex</i>Pneumonia, and Acquired Hemophagocytic Lymphohistiocytosis: A Deadly Association","year":2013,"lang":"en","type":"article","venue":"Case Reports in Pulmonology","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":7,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier de l’Université de Montréal; Hôpital du Sacré-Cœur de Montréal; Université de Montréal; Montreal Clinical Research Institute","funders":"","keywords":"Hemophagocytic lymphohistiocytosis; Medicine; Chronic granulomatous disease; Pneumonia; Burkholderia; Burkholderia cepacia complex; Immunology; Histiocytosis; Disease; Pediatrics; Pathology; Internal medicine; Biology; Bacteria","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005285915,0.001011286,0.0005484539,0.001297158,0.001692759,0.001222137,0.0007540351,0.003267698,0.003912125],"category_scores_gemma":[0.003051069,0.0006909829,0.0004060293,0.0006989054,0.001928254,0.001849131,0.001187511,0.002067559,0.0006477454],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004063559,"about_ca_system_score_gemma":0.0005077029,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009766133,"about_ca_topic_score_gemma":0.001120218,"domain_scores_codex":[0.9992066,0.0001539432,0.0001125046,0.0001741303,0.0000989396,0.0002537815],"domain_scores_gemma":[0.9971506,0.0009091544,0.0009775603,0.0002323283,0.0001301703,0.0006002087],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.0001122106,0.00006676982,0.1337982,0.00006325306,0.00002339839,0.8610486,0.0003120638,0.00003250051,0.001120875,0.0003065091,0.0004035662,0.002711994],"study_design_scores_gemma":[0.000007291577,0.00002815351,0.01641665,0.00001966185,0.00001298843,0.9825062,0.0001466648,0.00005643833,0.0001887675,0.0001436813,0.0004676151,0.000005983987],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9810822,0.009357426,0.001080336,0.001744945,0.0001712404,0.0000428879,0.0001005379,0.000062866,0.006357524],"genre_scores_gemma":[0.997007,0.001334151,0.0003121337,0.0003588772,0.0004611757,0.000007942992,0.00006810144,0.000006134474,0.0004445942],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003912125,"threshold_uncertainty_score":0.01308733,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01513695177223938,"score_gpt":0.2709372288365051,"score_spread":0.2558002770642657,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}