{"id":"W2062499657","doi":"10.1155/2013/874197","title":"Undiagnosed Chronic Granulomatous Disease,<i>Burkholderia cepacia complex</i>Pneumonia, and Acquired Hemophagocytic Lymphohistiocytosis: A Deadly Association","year":2013,"lang":"en","type":"article","venue":"Case Reports in Pulmonology","topic":"Autoimmune and Inflammatory Disorders Research","field":"Medicine","cited_by":7,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier de l’Université de Montréal; Hôpital du Sacré-Cœur de Montréal; Université de Montréal; Montreal Clinical Research Institute","funders":"","keywords":"Hemophagocytic lymphohistiocytosis; Medicine; Chronic granulomatous disease; Pneumonia; Burkholderia; Burkholderia cepacia complex; Immunology; Histiocytosis; Disease; Pediatrics; Pathology; Internal medicine; Biology; Bacteria","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0004329682,0.0002996259,0.0007405169,0.0003522083,0.0001899684,0.0000665987,0.00006680717,0.0003140552,0.0004735274],"category_scores_gemma":[0.000753458,0.0002991435,0.0001192533,0.0003381243,0.0002413331,0.0002359458,0.000125135,0.0002322821,0.0001001975],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001365629,"about_ca_system_score_gemma":0.000756087,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008301477,"about_ca_topic_score_gemma":0.0001415779,"domain_scores_codex":[0.9971584,0.0001737287,0.0009559686,0.0006356575,0.000315307,0.0007609176],"domain_scores_gemma":[0.9983422,0.0001675013,0.0003159696,0.0006630029,0.0001909045,0.000320433],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002213973,0.0006549201,0.6096935,0.0007728949,0.0002920601,0.3186443,0.0004509995,0.00003403425,0.04516901,0.0001731062,0.004147048,0.01974672],"study_design_scores_gemma":[0.003619086,0.0003893414,0.9074005,0.0002012132,0.0001980221,0.07247646,0.0004383553,0.004006088,0.001005388,0.001374517,0.008334761,0.0005563004],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9911104,0.004869949,0.00002046566,0.001479191,0.0002144979,0.001312984,0.000006279462,0.0001407225,0.0008454373],"genre_scores_gemma":[0.9975954,0.0005644024,0.00006058746,0.0003540819,0.00008382378,0.0005244437,0.00008372324,0.00005025648,0.0006832963],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.2977069,"threshold_uncertainty_score":0.9999461,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01513695177223938,"score_gpt":0.2709372288365051,"score_spread":0.2558002770642657,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}