{"id":"W2062718287","doi":"10.1165/rcmb.2008-0279oc","title":"Cystic Fibrosis Fatty Acid Imbalance Is Linked to Ceramide Deficiency and Corrected by Fenretinide","year":2008,"lang":"en","type":"article","venue":"American Journal of Respiratory Cell and Molecular Biology","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":99,"is_retracted":false,"has_abstract":true,"ca_institutions":"Cystic Fibrosis Canada; McGill University Health Centre; McGill University","funders":"National Institutes of Health","keywords":"Fenretinide; Ceramide; Docosahexaenoic acid; Cystic fibrosis; Internal medicine; Endocrinology; Arachidonic acid; Sphingomyelin; Sphingolipid; Medicine; Fatty acid; Chemistry; Cholesterol; Biochemistry; Retinoid; Apoptosis; Polyunsaturated fatty acid; Enzyme; Retinoic acid","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.000153384,0.0003294418,0.000572373,0.0005246634,0.0002765935,0.0001917682,0.0001403407,0.0003987071,0.0006642925],"category_scores_gemma":[0.0003418294,0.0001414803,0.0002925737,0.0002148199,0.0002366955,0.0001686601,0.0002239453,0.0004912557,0.0001362269],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001947745,"about_ca_system_score_gemma":0.0001636038,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0006374533,"about_ca_topic_score_gemma":0.0006781133,"domain_scores_codex":[0.9998154,0.00004495004,0.00002836724,0.00004364305,0.00003755498,0.00003013888],"domain_scores_gemma":[0.9997768,0.00003002206,0.000101208,0.0000152739,0.00002437787,0.00005236858],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.002233768,0.00007506737,0.01076723,0.00007091346,0.00004293684,0.001097199,0.00007943468,0.00004987991,0.9767588,0.00004426754,0.00006289695,0.008717474],"study_design_scores_gemma":[0.0002871142,0.003748826,0.3034331,0.0000631352,0.000255358,0.01395836,0.0003220603,0.001080719,0.6715045,0.0002584843,0.005050968,0.00003739114],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.997063,0.001948333,0.0004736003,0.00006274851,0.00001136611,0.00001337073,0.00007571182,0.00002674886,0.0003250475],"genre_scores_gemma":[0.9980526,0.0008093937,0.0006152075,0.00005360684,0.00001028577,0.00001827328,0.0001163896,0.000006871276,0.0003173852],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0006642925,"threshold_uncertainty_score":0.0022223,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008387681494614009,"score_gpt":0.2792642581936828,"score_spread":0.2708765766990688,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}