{"id":"W2063710124","doi":"10.1164/rccm.201002-0271oc","title":"Hereditary Pulmonary Alveolar Proteinosis: Pathogenesis, Presentation, Diagnosis, and Therapy","year":2010,"lang":"en","type":"article","venue":"American Journal of Respiratory and Critical Care Medicine","topic":"Neonatal Respiratory Health Research","field":"Medicine","cited_by":178,"is_retracted":false,"has_abstract":true,"ca_institutions":"University Hospital Foundation","funders":"National Center for Research Resources; National Heart, Lung, and Blood Institute; Cincinnati Children's Hospital Medical Center","keywords":"Medicine; Pulmonary alveolar proteinosis; Missense mutation; Immunology; Pathology; Asymptomatic; Nonsense mutation; Internal medicine; Lung; Mutation; Gene; Genetics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002059695,0.0006572771,0.0003225275,0.000384764,0.0002971103,0.000317085,0.000321511,0.0009167259,0.0009758092],"category_scores_gemma":[0.0005905404,0.0001576018,0.0001699059,0.000236259,0.0005420173,0.0003400842,0.0002846718,0.0005859338,0.0002962157],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003486894,"about_ca_system_score_gemma":0.0003506118,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004209579,"about_ca_topic_score_gemma":0.0003531523,"domain_scores_codex":[0.9998556,0.00003355637,0.00002127366,0.00003847455,0.00001940254,0.00003166558],"domain_scores_gemma":[0.9997829,0.00007193168,0.00005898881,0.000006913239,0.00001503313,0.00006432596],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0007091334,0.0003763881,0.6675172,0.0003634525,0.00005010541,0.2388287,0.0003335132,0.0009278602,0.04584984,0.0009295089,0.001535454,0.04257887],"study_design_scores_gemma":[0.00007209686,0.0007029506,0.1749334,0.0001324257,0.00005417921,0.8105761,0.0003036545,0.001854938,0.007177926,0.000662907,0.003509309,0.00002021952],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9830445,0.01094423,0.001579319,0.001352505,0.00003973589,0.00004895832,0.0001253346,0.0001051534,0.002760222],"genre_scores_gemma":[0.9968111,0.001551927,0.0009405871,0.0001174116,0.0001589447,0.00001608437,0.0001128021,0.000006816859,0.0002842018],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0009758092,"threshold_uncertainty_score":0.003264427,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03453079719898289,"score_gpt":0.3799479979546061,"score_spread":0.3454172007556232,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}