{"id":"W2065579584","doi":"10.1159/000166782","title":"The Various Renal Manifestations of the Nephropathic Form of Cystinosis","year":2008,"lang":"en","type":"article","venue":"American Journal of Nephrology","topic":"Biomedical Research and Pathophysiology","field":"Medicine","cited_by":34,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Children's Hospital","funders":"","keywords":"Medicine; Fanconi syndrome; Cystinosis; Nephrogenic diabetes insipidus; Tubulopathy; Hypoaldosteronism; Metabolic acidosis; Hyperkalemia; Bartter syndrome; Hyponatremia; Internal medicine; Pediatrics; Renal tubular acidosis; Distal renal tubular acidosis; Endocrinology; Diabetes insipidus; Acidosis; Kidney disease; Kidney; Hypokalemia; Blood pressure","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["sts"],"consensus_categories":[],"category_scores_codex":[0.0004649209,0.00008234815,0.0004054552,0.0001010894,0.0001369529,0.000001353607,0.0003018959,0.00005644329,0.00003264454],"category_scores_gemma":[0.0006516411,0.00003959493,0.0002058955,0.0003990393,0.003365987,0.00002577147,0.00006180161,0.0004927929,0.000002886117],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002481449,"about_ca_system_score_gemma":0.0006257709,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001333455,"about_ca_topic_score_gemma":0.00001738468,"domain_scores_codex":[0.9984157,0.0003089275,0.0005501124,0.00007947288,0.000381955,0.0002637952],"domain_scores_gemma":[0.9976248,0.0008675954,0.0007127964,0.0002509034,0.0003965926,0.0001473156],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.009181704,0.001096286,0.05186039,0.0001105692,0.001359433,0.001972144,0.005062795,0.0000287815,0.668357,0.001946529,0.0208472,0.2381772],"study_design_scores_gemma":[0.001862183,0.01492742,0.9319974,0.00008242069,0.0001985683,0.01814945,0.0005265331,0.0001313734,0.002079186,0.003002297,0.02695314,0.00009002765],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9903942,0.0003107573,0.0004479173,0.008409316,0.00009424892,0.00009994566,0.000006501969,0.000002524491,0.0002346013],"genre_scores_gemma":[0.9961879,0.001105796,0.0007369769,0.00174203,0.0001581517,0.000002631209,9.142642e-7,0.000007724742,0.00005782338],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.880137,"threshold_uncertainty_score":0.9993463,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0162183863725142,"score_gpt":0.2808543446923201,"score_spread":0.2646359583198059,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}