{"id":"W2065579584","doi":"10.1159/000166782","title":"The Various Renal Manifestations of the Nephropathic Form of Cystinosis","year":2008,"lang":"en","type":"article","venue":"American Journal of Nephrology","topic":"Biomedical Research and Pathophysiology","field":"Medicine","cited_by":34,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Children's Hospital","funders":"","keywords":"Medicine; Fanconi syndrome; Cystinosis; Nephrogenic diabetes insipidus; Tubulopathy; Hypoaldosteronism; Metabolic acidosis; Hyperkalemia; Bartter syndrome; Hyponatremia; Internal medicine; Pediatrics; Renal tubular acidosis; Distal renal tubular acidosis; Endocrinology; Diabetes insipidus; Acidosis; Kidney disease; Kidney; Hypokalemia; Blood pressure","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002227192,0.0003820604,0.0002837051,0.0008896692,0.0003111532,0.0002769238,0.0001884074,0.0002930813,0.001271061],"category_scores_gemma":[0.001029014,0.0002366513,0.0001940035,0.00042614,0.0004978148,0.0003479686,0.0004039784,0.0003237493,0.0001622689],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001628831,"about_ca_system_score_gemma":0.0001888207,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0004667719,"about_ca_topic_score_gemma":0.0008455701,"domain_scores_codex":[0.9998196,0.00003623859,0.00002930163,0.00002269954,0.0000496161,0.00004265794],"domain_scores_gemma":[0.9996802,0.00009124334,0.00008340698,0.00002445393,0.00003274005,0.00008798207],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001056104,0.0002306145,0.4997349,0.000428829,0.0001742956,0.2464071,0.002171956,0.0009462112,0.1267087,0.004437193,0.001666197,0.1160379],"study_design_scores_gemma":[0.00004920489,0.0003016671,0.4312225,0.00004753908,0.00006656679,0.5500706,0.00043625,0.0004707469,0.01191637,0.001610502,0.003776749,0.0000312842],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9864668,0.001420996,0.00158476,0.0001543895,0.000007615219,0.0000317738,0.000135871,0.00007981142,0.01011795],"genre_scores_gemma":[0.998128,0.0006095265,0.0006776917,0.00006979487,0.00001688094,0.000008290105,0.00005560045,0.000007906356,0.0004262711],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001271061,"threshold_uncertainty_score":0.004252136,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0162183863725142,"score_gpt":0.2808543446923201,"score_spread":0.2646359583198059,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}