{"id":"W2068816428","doi":"10.1212/wnl.56.3.336","title":"Assessment of a disease-specific muscular impairment rating scale in myotonic dystrophy","year":2001,"lang":"en","type":"article","venue":"Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":377,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre Hospitalier de l’Université de Montréal","funders":"","keywords":"Myotonic dystrophy; Muscular dystrophy; Rating scale; Physical medicine and rehabilitation; Medicine; Disease; Neuromuscular disease; Physical therapy; Psychology; Internal medicine; Developmental psychology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001171606,0.0001997432,0.0002711526,0.0001910673,0.00007315211,0.00001886906,0.0003157238,0.00004643252,0.0001643709],"category_scores_gemma":[0.00009375529,0.00019702,0.0001151198,0.0004059028,0.000196062,0.00006501444,0.0001419539,0.0002212863,0.00001867919],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00002718337,"about_ca_system_score_gemma":0.0001026039,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001149183,"about_ca_topic_score_gemma":0.0000144025,"domain_scores_codex":[0.9974664,0.0006286306,0.000397968,0.0007235924,0.0003449453,0.0004383938],"domain_scores_gemma":[0.9989927,0.0001634189,0.0001356289,0.0005073045,0.00003469414,0.0001662814],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0002517231,0.0006371695,0.1974587,0.00002502171,0.000002191608,0.0003169411,0.00004860289,0.00766946,0.7924834,0.0007452373,0.00004120768,0.0003202614],"study_design_scores_gemma":[0.001041992,0.001096389,0.9104839,0.000008047936,0.0000117929,0.0000245662,0.00000664428,0.004430752,0.08142542,0.0002920153,0.00100143,0.0001770681],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9976273,0.00007403791,0.0002273587,0.0006541648,0.0002682789,0.0004897764,0.00001524472,0.00004036854,0.0006035002],"genre_scores_gemma":[0.9982107,0.0001857966,0.0001725563,0.001222016,0.00005174729,0.0001053869,0.000002754262,0.00002771504,0.00002136228],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.7130252,"threshold_uncertainty_score":0.8034241,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02293268131362515,"score_gpt":0.2777772417186982,"score_spread":0.254844560405073,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}