{"id":"W2075186362","doi":"10.1038/emboj.2010.143","title":"ALS‐associated fused in sarcoma (FUS) mutations disrupt Transportin‐mediated nuclear import","year":2010,"lang":"en","type":"article","venue":"The EMBO Journal","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":836,"is_retracted":false,"has_abstract":false,"ca_institutions":"Vancouver General Hospital","funders":"Canadian Institutes of Health Research; Hans und Ilse Breuer-Stiftung; Stavros Niarchos Foundation","keywords":"Biology; Nuclear transport; Frontotemporal lobar degeneration; Nuclear localization sequence; NLS; Amyotrophic lateral sclerosis; Stress granule; Pathogenesis; Neurodegeneration; Nuclear export signal; Cytoplasm; Cell nucleus; Cell biology; Genetics; Pathology; Frontotemporal dementia; Gene; Disease; Immunology; Medicine","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01914000375676064,"score_gpt":0.2988321649389096,"score_spread":0.279692161182149,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}