{"id":"W2076100327","doi":"10.1182/blood-2008-09-179630","title":"FAS-L, IL-10, and double-negative CD4- CD8- TCR alpha/beta+ T cells are reliable markers of autoimmune lymphoproliferative syndrome (ALPS) associated with FAS loss of function.","year":2009,"lang":"en","type":"preprint","venue":"PubMed","topic":"Lymphoma Diagnosis and Treatment","field":"Medicine","cited_by":124,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"Institut National de la Santé et de la Recherche Médicale","keywords":"Autoimmune lymphoproliferative syndrome; Hypergammaglobulinemia; CD8; Immunology; Apoptosis; Cytotoxic T cell; Autoimmunity; Fas receptor; T cell; Lymphoproliferative disorders; In vitro; Biology; Molecular biology; Antigen; Immune system; Antibody; Programmed cell death; Genetics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.000629741,0.000787852,0.002193288,0.0003653446,0.0001193885,0.00005918934,0.0002170373,0.000610723,0.0001247728],"category_scores_gemma":[0.0001278409,0.0006112681,0.0003421402,0.0004697435,0.0004097767,0.0001563458,0.0002663152,0.0003855325,0.000009238172],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001033305,"about_ca_system_score_gemma":0.0004902689,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007115389,"about_ca_topic_score_gemma":0.00005502617,"domain_scores_codex":[0.9961853,0.0001641736,0.001026074,0.001012139,0.0008823884,0.0007299414],"domain_scores_gemma":[0.9961038,0.0002825239,0.001613039,0.0008609497,0.0008005496,0.0003391911],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.05140531,0.02166256,0.7902043,0.005860896,0.05603404,0.003922761,0.003885413,0.002768171,0.0003878547,0.0008836184,0.02291417,0.04007095],"study_design_scores_gemma":[0.01636634,0.001136007,0.9644234,0.001640731,0.002529513,0.00009024086,0.0003022362,0.00007682795,0.01238683,0.0002200447,0.0002884136,0.0005394045],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9845534,0.002414761,0.00002320829,0.0006941179,0.0003853429,0.005158893,0.0007062629,0.0001276121,0.005936389],"genre_scores_gemma":[0.9911272,0.0008507062,0.0002684453,0.0001569347,0.00004781334,0.002675341,0.0003856988,0.00007943033,0.004408464],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1742191,"threshold_uncertainty_score":0.9996338,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01669519722641661,"score_gpt":0.2165951753414617,"score_spread":0.1998999781150451,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}