{"id":"W2077235837","doi":"10.1016/j.artres.2008.08.309","title":"P1.01 TREATMENT WITH DEXAMETHASONE REVERSES IMPARED ELASTOGENESIS AND COLLAGENOGENESIS IN CULTURES OF FIBROBLASTS FROM PATIENTS WITH LOEYS-DIETZ SYNDROME (LDS)","year":2008,"lang":"en","type":"article","venue":"Artery Research","topic":"Genetic Syndromes and Imprinting","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hospital for Sick Children","funders":"","keywords":"Medicine; Dexamethasone; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001450211,0.0001983404,0.0002905395,0.0001234209,0.000126121,0.00001876463,0.0001452441,0.0001078936,0.00003311133],"category_scores_gemma":[0.00003051441,0.0001426619,0.00004089532,0.0002773874,0.0002597017,0.000008464955,0.0001237644,0.0000629766,0.000004615063],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00004058839,"about_ca_system_score_gemma":0.0001314745,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008013573,"about_ca_topic_score_gemma":0.000700484,"domain_scores_codex":[0.9983436,0.0001633613,0.000226264,0.0004989895,0.0003488832,0.0004189029],"domain_scores_gemma":[0.9991911,0.00006197733,0.00006939336,0.0003880281,0.000161789,0.0001277249],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0003327553,0.0002821066,0.8376716,0.00002791619,0.0001924402,0.00004150943,0.0004742265,0.00006179506,0.158862,3.553706e-7,0.000123041,0.001930275],"study_design_scores_gemma":[0.00236271,0.004294592,0.9053004,0.00008232517,0.00002077205,0.00009859788,0.0004618953,0.00001395181,0.08670952,0.000004287279,0.0004541375,0.0001968476],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9985752,0.0007951268,0.00002808089,0.00003204936,0.00001393148,0.0004140261,0.00005009634,0.000005077866,0.00008641527],"genre_scores_gemma":[0.9971866,0.0006231318,0.001725871,0.00001200865,0.00002025859,0.00005377395,0.00006883166,0.00002969217,0.0002798043],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.07215247,"threshold_uncertainty_score":0.5817586,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02711041844936865,"score_gpt":0.2762683297107883,"score_spread":0.2491579112614196,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}