{"id":"W2078439332","doi":"10.1016/j.pediatrneurol.2007.11.005","title":"Congenital Axonal Neuropathy and Encephalopathy","year":2008,"lang":"en","type":"article","venue":"Pediatric Neurology","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":8,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hôpital Charles-Le Moyne; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"","keywords":"Medicine; Hypotonia; Pathology; Encephalopathy; Atrophy; Sural nerve; Ataxia; Pediatrics; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow"],"consensus_categories":[],"category_scores_codex":[0.0000947607,0.0002684014,0.0002708689,0.0001818471,0.0002884425,0.00001645608,0.0003683421,0.0001476633,0.0002195901],"category_scores_gemma":[0.001404629,0.0002502477,0.00007466796,0.0004543821,0.0005582885,0.0001971219,0.0002482083,0.0005818704,0.000364625],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000003580653,"about_ca_system_score_gemma":0.00005733743,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000009162543,"about_ca_topic_score_gemma":0.000002166966,"domain_scores_codex":[0.9973139,0.0004692038,0.0003263434,0.0009405394,0.0003188362,0.0006311992],"domain_scores_gemma":[0.9983522,0.0009761796,0.00009570409,0.0002825989,0.00002638472,0.0002669083],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0009031856,0.0008675655,0.8950433,0.0000434735,0.000007713666,0.02560777,0.0005940234,0.0001118236,0.06173272,0.002963976,0.008402464,0.003721976],"study_design_scores_gemma":[0.003010113,0.004865376,0.943097,4.644762e-7,0.00007651401,0.01526953,0.000009366663,0.001459739,0.002865832,0.003280257,0.0249533,0.001112518],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9934139,0.0002133263,0.00003692309,0.001561808,0.0008535016,0.0002347387,0.00002304319,0.0002511709,0.003411557],"genre_scores_gemma":[0.9850056,0.001332633,0.00002700797,0.01298821,0.0005116944,0.00002640187,0.000001520632,0.00003242497,0.00007456494],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.05886689,"threshold_uncertainty_score":0.999995,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03272043841525372,"score_gpt":0.2214534135749279,"score_spread":0.1887329751596742,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}