{"id":"W2078439332","doi":"10.1016/j.pediatrneurol.2007.11.005","title":"Congenital Axonal Neuropathy and Encephalopathy","year":2008,"lang":"en","type":"article","venue":"Pediatric Neurology","topic":"Hereditary Neurological Disorders","field":"Neuroscience","cited_by":8,"is_retracted":false,"has_abstract":false,"ca_institutions":"Hôpital Charles-Le Moyne; Université de Montréal; Centre Hospitalier Universitaire Sainte-Justine","funders":"","keywords":"Medicine; Hypotonia; Pathology; Encephalopathy; Atrophy; Sural nerve; Ataxia; Pediatrics; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002370639,0.0007523474,0.00045121,0.001709656,0.001313827,0.0008859269,0.0005930476,0.001820681,0.01150353],"category_scores_gemma":[0.001162444,0.0003036333,0.0002723921,0.001206149,0.001502635,0.001160309,0.001004016,0.001273458,0.001119333],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0008373836,"about_ca_system_score_gemma":0.0008655718,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003363553,"about_ca_topic_score_gemma":0.00556682,"domain_scores_codex":[0.999762,0.00002906788,0.0000265889,0.0000402258,0.00004482329,0.00009727123],"domain_scores_gemma":[0.9993704,0.000261762,0.0001263697,0.00004739361,0.00005838521,0.0001356674],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.0001367806,0.00006601018,0.02091289,0.0001134182,0.00003490518,0.9524469,0.0002052826,0.0001932305,0.001467677,0.008135847,0.003694687,0.0125925],"study_design_scores_gemma":[0.00002210084,0.00006179888,0.0247902,0.00004206592,0.00004105272,0.9652643,0.0001940019,0.0002123404,0.001075931,0.003184999,0.005099164,0.00001206963],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.7629331,0.01306789,0.001789855,0.005522472,0.0007327318,0.00005938663,0.0005299508,0.000268067,0.2150964],"genre_scores_gemma":[0.9740624,0.00370423,0.001033714,0.0007977683,0.0009126053,0.00001594848,0.0001798096,0.0000391353,0.01925433],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01150353,"threshold_uncertainty_score":0.03848308,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03272043841525372,"score_gpt":0.2214534135749279,"score_spread":0.1887329751596742,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}