{"id":"W2082823926","doi":"10.1212/01.wnl.0000258678.58808.86","title":"Autosomal dominant primary lateral sclerosis","year":2007,"lang":"en","type":"article","venue":"Neurology","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":30,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hôpital de l'Enfant-Jésus","funders":"","keywords":"Multiple sclerosis; Medicine; Primary (astronomy); Neuroscience; Physical medicine and rehabilitation; Biology; Physics; Immunology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002336205,0.001310708,0.0004081139,0.0008954612,0.001502482,0.0004991652,0.0003574743,0.000596929,0.01264121],"category_scores_gemma":[0.0005419019,0.0001597131,0.000264445,0.0007111155,0.0005427255,0.0002594841,0.0003864508,0.0002815988,0.002064786],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001449357,"about_ca_system_score_gemma":0.001538574,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.04540167,"about_ca_topic_score_gemma":0.09409038,"domain_scores_codex":[0.9996886,0.00003329358,0.00001171059,0.00006220047,0.0001223319,0.00008182487],"domain_scores_gemma":[0.9997719,0.00004686989,0.00004269771,0.00002143544,0.00006957998,0.00004759218],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.001171512,0.0003029135,0.1326124,0.001110806,0.0003387882,0.520375,0.002910269,0.0005914352,0.1130842,0.01710466,0.03647142,0.1739265],"study_design_scores_gemma":[0.0001380824,0.0002735191,0.1658067,0.0002241225,0.000293745,0.7091945,0.0006201258,0.0008872474,0.007242573,0.00259728,0.1126579,0.00006421014],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.7677084,0.01119232,0.00672393,0.002415102,0.0003198789,0.0006470695,0.00449975,0.001310469,0.2051831],"genre_scores_gemma":[0.9539658,0.002433524,0.002485899,0.0008422761,0.0001119724,0.00007722282,0.0007951909,0.00007911354,0.03920898],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.04540167,"threshold_uncertainty_score":0.09027481,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03075237006346781,"score_gpt":0.2842077416446838,"score_spread":0.2534553715812159,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}