{"id":"W2082972113","doi":"10.1007/s00401-009-0598-9","title":"FUS pathology in basophilic inclusion body disease","year":2009,"lang":"en","type":"article","venue":"Acta Neuropathologica","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":248,"is_retracted":false,"has_abstract":false,"ca_institutions":"Vancouver General Hospital; University of Toronto; St. Michael's Hospital","funders":"Canadian Institutes of Health Research","keywords":"Frontotemporal lobar degeneration; Amyotrophic lateral sclerosis; Pathology; Progressive supranuclear palsy; Cytoplasmic inclusion; Pick's disease; Frontotemporal dementia; Basophilic; Inclusion bodies; Motor neuron; Temporal cortex; Neurodegeneration; Biology; Degenerative disease; Atrophy; Medicine; Dementia; Disease; Neuroscience; Cytoplasm; Genetics; Gene","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004004606,0.0002234002,0.0003747595,0.0002225835,0.0001749626,0.00001814072,0.0002988928,0.0001388626,0.0002937107],"category_scores_gemma":[0.0009256488,0.0001630261,0.0001040978,0.0004402158,0.0001462978,0.0001054706,0.0006305887,0.000603176,0.0001281925],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00008431246,"about_ca_system_score_gemma":0.00006739064,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.000003599573,"about_ca_topic_score_gemma":6.727951e-7,"domain_scores_codex":[0.9976271,0.0003894771,0.0003410638,0.0006191314,0.0004290421,0.0005941803],"domain_scores_gemma":[0.9987772,0.00008623755,0.00006522968,0.0006379366,0.00006179154,0.0003715896],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.001207265,0.00107953,0.04912819,0.00002566981,0.000002812076,0.03714073,0.0002163617,0.000006874351,0.8942624,0.0003278471,0.0006219615,0.0159803],"study_design_scores_gemma":[0.001117619,0.001249068,0.9931099,0.00004295783,0.00001506588,0.0003311765,0.000003839767,0.0002124261,0.0003088208,0.001857667,0.00159742,0.0001540495],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9720423,0.0002157168,0.000007822602,0.02396912,0.0000806787,0.0005035821,0.000005739643,0.0001447978,0.0030302],"genre_scores_gemma":[0.9910985,0.0004530182,0.000148925,0.0077209,0.0001439761,0.00002265177,0.00002454062,0.00002114549,0.0003662983],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.9439817,"threshold_uncertainty_score":0.6648009,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02376201456843462,"score_gpt":0.2995688577493403,"score_spread":0.2758068431809057,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}