{"id":"W2082972113","doi":"10.1007/s00401-009-0598-9","title":"FUS pathology in basophilic inclusion body disease","year":2009,"lang":"en","type":"article","venue":"Acta Neuropathologica","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":248,"is_retracted":false,"has_abstract":false,"ca_institutions":"Vancouver General Hospital; University of Toronto; St. Michael's Hospital","funders":"Canadian Institutes of Health Research","keywords":"Frontotemporal lobar degeneration; Amyotrophic lateral sclerosis; Pathology; Progressive supranuclear palsy; Cytoplasmic inclusion; Pick's disease; Frontotemporal dementia; Basophilic; Inclusion bodies; Motor neuron; Temporal cortex; Neurodegeneration; Biology; Degenerative disease; Atrophy; Medicine; Dementia; Disease; Neuroscience; Cytoplasm; Genetics; Gene","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0007743218,0.0008162545,0.0003869699,0.003521729,0.001053258,0.0009259524,0.0003180102,0.00117633,0.00373882],"category_scores_gemma":[0.001281085,0.000422438,0.0002258132,0.0008498613,0.001358994,0.001357357,0.0007588182,0.0003708372,0.0006289758],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004113253,"about_ca_system_score_gemma":0.0002097708,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0009917869,"about_ca_topic_score_gemma":0.0007063578,"domain_scores_codex":[0.9997948,0.00003660438,0.00003457099,0.00002469766,0.00005115434,0.00005828031],"domain_scores_gemma":[0.9994748,0.000190619,0.0001230428,0.00004720292,0.0000847037,0.00007960895],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.005939955,0.0001568057,0.1793038,0.0006362254,0.0003209961,0.4612483,0.002547044,0.0009036556,0.294497,0.005612697,0.002175533,0.04665787],"study_design_scores_gemma":[0.0001279575,0.0006178892,0.26917,0.0001656529,0.0003277797,0.6504555,0.002035418,0.002879581,0.057968,0.009241437,0.006939524,0.00007143104],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9879366,0.003967723,0.0008796853,0.0002073888,0.00005494589,0.00000892073,0.00009636281,0.00006086621,0.006787343],"genre_scores_gemma":[0.9986582,0.0005815842,0.0002665822,0.00001610872,0.00003663648,0.000002964287,0.00003742526,0.000005140746,0.0003952619],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00373882,"threshold_uncertainty_score":0.01250762,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02376201456843462,"score_gpt":0.2995688577493403,"score_spread":0.2758068431809057,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}