{"id":"W2084907056","doi":"10.1212/wnl.57.4.658","title":"Clinical markers of early disease in persons near onset of Huntington’s disease","year":2001,"lang":"en","type":"article","venue":"Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":205,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"National Institute of Neurological Disorders and Stroke; National Institute of Mental Health","keywords":"Disease; Huntington's disease; Neuropsychology; Cognition; Rating scale; Medicine; Longitudinal study; Cognitive decline; Psychology; Internal medicine; Clinical psychology; Psychiatry; Pathology; Developmental psychology; Dementia","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005687878,0.0004236034,0.0004313808,0.001015057,0.0005233632,0.0006060954,0.0002237517,0.0007758482,0.00126683],"category_scores_gemma":[0.002733771,0.0001967071,0.0001994549,0.0006271549,0.0002614816,0.0004583697,0.0004250359,0.0005969017,0.0003351251],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001978747,"about_ca_system_score_gemma":0.0002498706,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002135798,"about_ca_topic_score_gemma":0.002694041,"domain_scores_codex":[0.9997168,0.00008839607,0.00003617103,0.00005917095,0.0000575405,0.00004178622],"domain_scores_gemma":[0.998499,0.0003269708,0.0006422379,0.00003948437,0.0001747668,0.0003175505],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002358772,0.00009039574,0.9971491,0.00001397856,0.00001672688,0.0002087569,0.00006830617,0.00005215832,0.0004512317,0.00001367614,0.0001025614,0.001597212],"study_design_scores_gemma":[0.00000883334,0.0002862708,0.9986343,0.000007482487,0.00001559657,0.0005988049,0.0000810816,0.00008098616,0.0001317611,0.00002338363,0.0001281999,0.000003243882],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9983967,0.0004553215,0.00008825038,0.00004923565,0.000008620775,0.00001857685,0.0002043427,0.000006426787,0.0007727075],"genre_scores_gemma":[0.9990062,0.0001252831,0.0002180507,0.00002996969,0.00001424381,0.00001268409,0.0003312925,9.73217e-7,0.0002613239],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002135798,"threshold_uncertainty_score":0.004246771,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03633564772539107,"score_gpt":0.3139062863650646,"score_spread":0.2775706386396736,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}