{"id":"W2084907056","doi":"10.1212/wnl.57.4.658","title":"Clinical markers of early disease in persons near onset of Huntington’s disease","year":2001,"lang":"en","type":"article","venue":"Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":205,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"National Institute of Neurological Disorders and Stroke; National Institute of Mental Health","keywords":"Disease; Huntington's disease; Neuropsychology; Cognition; Rating scale; Medicine; Longitudinal study; Cognitive decline; Psychology; Internal medicine; Clinical psychology; Psychiatry; Pathology; Developmental psychology; Dementia","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001872614,0.0001842534,0.0003481498,0.0001494533,0.0000531351,0.00001174627,0.0004119254,0.00006378642,0.0001622865],"category_scores_gemma":[0.002604653,0.0001893,0.0002032245,0.0003681575,0.000838562,0.00006925141,0.0001552157,0.0002574198,0.00002694054],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000005188062,"about_ca_system_score_gemma":0.0002329544,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00008517713,"about_ca_topic_score_gemma":0.00002944807,"domain_scores_codex":[0.9969602,0.001090308,0.0005902067,0.0006880991,0.0002848429,0.0003863857],"domain_scores_gemma":[0.9979995,0.0007707718,0.000226915,0.0005725626,0.0000451061,0.0003851517],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.004077135,0.0005639807,0.9854168,0.00002366906,0.000003225217,0.0002078352,0.00004743553,0.0004148311,0.008587512,0.0001040101,0.0001815196,0.0003719944],"study_design_scores_gemma":[0.0007605336,0.0008011882,0.9925349,0.000008314308,0.00003393663,0.000002430013,0.000002863661,0.0009226543,0.004125566,0.000183779,0.0004981137,0.0001256851],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9978444,0.0000326294,0.000009470758,0.00109,0.0003095748,0.000300049,0.0001417451,0.00002795699,0.0002441615],"genre_scores_gemma":[0.9975676,0.0000680509,0.0000367363,0.002165916,0.00003818281,0.00002161159,0.000003272814,0.00002850154,0.00007011186],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.007118084,"threshold_uncertainty_score":0.771943,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03633564772539107,"score_gpt":0.3139062863650646,"score_spread":0.2775706386396736,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}