{"id":"W2085910454","doi":"10.1016/j.pediatrneurol.2008.11.020","title":"Early-Onset Neurodegenerative Disease of the Cerebellum and Motor Axons","year":2009,"lang":"en","type":"article","venue":"Pediatric Neurology","topic":"Neurological diseases and metabolism","field":"Neuroscience","cited_by":4,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Manitoba","funders":"","keywords":"Atrophy; Medicine; Cerebellum; Spinal cord; Brainstem; Motor neuron; White matter; Cerebellar vermis; Pathology; Degenerative disease; Central nervous system disease; Disease; Magnetic resonance imaging; Surgery; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003761734,0.001194293,0.0007930089,0.001093151,0.0006258696,0.0008400549,0.0006562339,0.001095374,0.00372508],"category_scores_gemma":[0.001174665,0.0004448213,0.0003308503,0.0006537769,0.0008057169,0.0008397096,0.0006238825,0.0009120322,0.0007064665],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0008342377,"about_ca_system_score_gemma":0.001194883,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.006835062,"about_ca_topic_score_gemma":0.01039362,"domain_scores_codex":[0.9996724,0.00003881508,0.00003083911,0.00006719564,0.00008561992,0.000105183],"domain_scores_gemma":[0.9992888,0.0001498954,0.0002442305,0.00004590728,0.0001230515,0.0001481196],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.001086777,0.0002810977,0.2012391,0.0005458844,0.0001772687,0.6612681,0.0005659157,0.0006087802,0.09016445,0.004150925,0.002774406,0.03713727],"study_design_scores_gemma":[0.00005137458,0.0003100365,0.3429595,0.0001225835,0.0001661013,0.6346506,0.0003262909,0.0004468691,0.01577083,0.001406993,0.003763279,0.00002548753],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9665169,0.008485089,0.003724005,0.0006328934,0.00008195292,0.00006470545,0.0006074632,0.0001561992,0.01973084],"genre_scores_gemma":[0.9923249,0.001795097,0.001894806,0.0001146567,0.00007706021,0.00001067528,0.0002230977,0.00002841516,0.003531211],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.006835062,"threshold_uncertainty_score":0.01359057,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01623577758945204,"score_gpt":0.233890224488499,"score_spread":0.2176544468990469,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}