{"id":"W2086847345","doi":"10.1001/archneur.61.1.122","title":"Fatal Familial Insomnia","year":2004,"lang":"en","type":"article","venue":"Archives of Neurology","topic":"Prion Diseases and Protein Misfolding","field":"Biochemistry, Genetics and Molecular Biology","cited_by":23,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of British Columbia","funders":"","keywords":"Fatal familial insomnia; Gliosis; Thalamus; Medicine; Myoclonus; Neuroscience; Ataxia; Pathology; Internal medicine; Psychology; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00002184841,0.00007719434,0.00008877659,0.00003494753,0.00003086692,0.000002598368,0.0001740697,0.00005067422,0.000009337617],"category_scores_gemma":[0.00004930572,0.00007638019,0.0000829779,0.00002623936,0.0001400523,0.0000014235,0.000138681,0.00006333357,0.000005554741],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":5.914033e-7,"about_ca_system_score_gemma":0.00004274294,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0000218541,"about_ca_topic_score_gemma":0.000009884502,"domain_scores_codex":[0.9994442,0.00003746715,0.0001180845,0.0002027824,0.00004466496,0.0001527791],"domain_scores_gemma":[0.9996722,0.00001361722,0.0000448542,0.0002071731,0.000007278799,0.00005492698],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0003879377,0.00005768957,0.002251672,0.0000104689,0.00001914476,0.00001191396,0.00003930058,0.0003254846,0.9784238,0.0009392158,0.00004989014,0.01748346],"study_design_scores_gemma":[0.003550743,0.003271207,0.1034637,0.00001489555,0.00002874825,0.0001201422,0.00002055616,0.00005864865,0.8004168,0.01768668,0.07099028,0.0003776244],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9961259,0.0008090248,0.001426643,0.0003929975,0.00008916565,0.00007983107,0.00001856061,0.00000781666,0.001050005],"genre_scores_gemma":[0.997951,0.000492799,0.0006837804,0.0006912018,0.0001145667,0.000006003821,0.00002948242,0.00001005912,0.00002114157],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.178007,"threshold_uncertainty_score":0.3114694,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.006426371248484384,"score_gpt":0.2277565915140962,"score_spread":0.2213302202656118,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}