{"id":"W2092986835","doi":"10.1111/j.1468-1331.2009.02622.x","title":"A longitudinal study of Taiwanese Sialidosis type 1: an insight into the concept of cherry‐red spot myoclonus syndrome","year":2009,"lang":"en","type":"article","venue":"European Journal of Neurology","topic":"Glycogen Storage Diseases and Myoclonus","field":"Medicine","cited_by":41,"is_retracted":false,"has_abstract":true,"ca_institutions":"Centre for Movement Disorders","funders":"National Science Council","keywords":"Myoclonus; Medicine; Somatosensory evoked potential; Ophthalmology; Pediatrics; Anesthesia","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005966167,0.00026618,0.0002049964,0.0007885461,0.0005362133,0.0004271923,0.0001875748,0.000443947,0.0008232657],"category_scores_gemma":[0.001733242,0.0001951308,0.0002869421,0.0005645028,0.0002529988,0.0004488178,0.0003271517,0.0004169372,0.0001799398],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003261782,"about_ca_system_score_gemma":0.0004006794,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005402333,"about_ca_topic_score_gemma":0.004027869,"domain_scores_codex":[0.9997732,0.00006989619,0.00002195577,0.00006040945,0.00002601128,0.00004861884],"domain_scores_gemma":[0.9988515,0.0001480625,0.0004080781,0.00008549872,0.0001811745,0.0003256585],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.00006173101,0.00002350475,0.9979995,0.000002251384,0.00001758906,0.000462076,0.0002128038,0.00001966354,0.0004779887,0.00001089445,0.00003973774,0.0006722415],"study_design_scores_gemma":[0.000005019776,0.0002014738,0.9976106,0.000005554479,0.0000211828,0.00143789,0.0002917593,0.0001454613,0.00008972805,0.00001943848,0.0001669874,0.000004953668],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9996403,0.00008013887,0.00004725583,0.00003032931,0.000002053083,0.00000363362,0.0000813907,0.000002100661,0.0001127831],"genre_scores_gemma":[0.9995885,0.0000513115,0.00005119498,0.00001786196,0.000004626472,0.000007030779,0.0001855869,0.000001318177,0.00009243535],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005402333,"threshold_uncertainty_score":0.01074177,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03268533770980468,"score_gpt":0.2880574959532505,"score_spread":0.2553721582434458,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}