{"id":"W2093405744","doi":"10.1007/s00401-012-1020-6","title":"Transportin 1 accumulates specifically with FET proteins but no other transportin cargos in FTLD-FUS and is absent in FUS inclusions in ALS with FUS mutations","year":2012,"lang":"en","type":"article","venue":"Acta Neuropathologica","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":86,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of British Columbia; Vancouver General Hospital; Health Sciences Centre; Sunnybrook Health Science Centre; London Health Sciences Centre; University of Toronto; St. Michael's Hospital","funders":"Canadian Institutes of Health Research","keywords":"Frontotemporal lobar degeneration; Biology; Amyotrophic lateral sclerosis; Pathology; TARDBP; Molecular biology; Frontotemporal dementia; Medicine; SOD1; Dementia","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003842514,0.0005248952,0.0006512009,0.001740689,0.0008883329,0.0007588476,0.0004566714,0.0008892408,0.002355506],"category_scores_gemma":[0.0005601339,0.0006013574,0.0003961777,0.0004858373,0.000761039,0.0009137936,0.0006239096,0.0006788226,0.0006554598],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006361185,"about_ca_system_score_gemma":0.000296654,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00131506,"about_ca_topic_score_gemma":0.001450726,"domain_scores_codex":[0.9996877,0.00003185062,0.00003639908,0.00007542842,0.00007932493,0.00008932174],"domain_scores_gemma":[0.9994962,0.0001105103,0.0001161231,0.00003722171,0.0000654252,0.0001744086],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.0004059762,0.00003688634,0.002919967,0.00006082098,0.00003406783,0.001668428,0.00009005027,0.00008381018,0.9933287,0.0002101702,0.0001253246,0.001035841],"study_design_scores_gemma":[0.00006203624,0.0003461735,0.130655,0.00003373672,0.0001445255,0.02130866,0.0003401892,0.001872381,0.840371,0.00113926,0.003689302,0.00003779668],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9956062,0.001704137,0.001114658,0.00009572458,0.00002856068,0.000006416047,0.0001552765,0.00005123582,0.001237649],"genre_scores_gemma":[0.9957801,0.0003685832,0.00100851,0.00006014638,0.00002163589,0.00001361331,0.0004481965,0.00004283678,0.002256382],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002355506,"threshold_uncertainty_score":0.007879972,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03966092861824076,"score_gpt":0.2909096188082894,"score_spread":0.2512486901900486,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}