{"id":"W2105713463","doi":"10.14740/jmc.v5i9.1900","title":"Perioperative Management of an Adolescent With Friedreich’s Ataxia and Hypertrophic Cardiomyopathy","year":2014,"lang":"en","type":"article","venue":"Journal of Medical Cases","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Medicine; Ataxia; Scoliosis; Perioperative; Spinal fusion; Cardiomyopathy; Orthopedic surgery; Pediatrics; Diabetes mellitus; Surgery; Internal medicine; Heart failure; Psychiatry; Endocrinology","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001967039,0.0006198511,0.0006494264,0.0007775715,0.001481779,0.0005181496,0.0004652576,0.001767008,0.00120038],"category_scores_gemma":[0.001190074,0.0002471584,0.0004326867,0.0003328101,0.0004916982,0.0008268546,0.0007751904,0.001962502,0.000335251],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005570509,"about_ca_system_score_gemma":0.0007023595,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008768293,"about_ca_topic_score_gemma":0.002256967,"domain_scores_codex":[0.9997982,0.00003184293,0.00003111152,0.00002898185,0.00004246435,0.00006742121],"domain_scores_gemma":[0.9996811,0.00005319914,0.00007830618,0.000007991764,0.00002364819,0.0001558671],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"case_report","study_design_scores_codex":[0.00002489024,0.0000719063,0.01808865,0.00003121965,0.000007948738,0.9758753,0.000178801,0.00008934899,0.0008627546,0.0003013898,0.0005355855,0.003932239],"study_design_scores_gemma":[0.000005674622,0.0001141408,0.006145026,0.00007127579,0.00001260849,0.9911467,0.0002805,0.0002358261,0.0004235656,0.000294221,0.001262403,0.000008054772],"study_design_candidate":"case_report","study_design_consensus":"case_report","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9634542,0.01315359,0.003959605,0.007309981,0.0005778288,0.0001184312,0.0001232556,0.0001053126,0.01119777],"genre_scores_gemma":[0.9902331,0.004336416,0.002298235,0.001389212,0.0004777246,0.0000290436,0.00007451069,0.00001319179,0.00114861],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001767008,"threshold_uncertainty_score":0.004041672,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02513506491824799,"score_gpt":0.2742930254366088,"score_spread":0.2491579605183608,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}