{"id":"W2112183923","doi":"10.1186/1471-2377-11-61","title":"Early diagnosis of peripheral nervous system involvement in Fabry disease and treatment of neuropathic pain: the report of an expert panel","year":2011,"lang":"en","type":"review","venue":"BMC Neurology","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":148,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; McGill University Health Centre","funders":"","keywords":"Fabry disease; Medicine; Neuropathic pain; Peripheral neuropathy; Neurology; Enzyme replacement therapy; Disease; Medical history; Globotriaosylceramide; Intensive care medicine; Pathology; Internal medicine; Diabetes mellitus; Anesthesia; Psychiatry","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.01851733,0.0006682121,0.000867268,0.001126089,0.001371278,0.001532026,0.001748847,0.00540977,0.001887917],"category_scores_gemma":[0.01992504,0.0003607188,0.00111713,0.0007201422,0.0006455886,0.001382884,0.002176696,0.003782305,0.001078356],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001391367,"about_ca_system_score_gemma":0.003828766,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002462915,"about_ca_topic_score_gemma":0.003326218,"domain_scores_codex":[0.9919457,0.003870223,0.001189229,0.0005931829,0.001414337,0.0009872988],"domain_scores_gemma":[0.9836739,0.003441418,0.001039828,0.0004293663,0.008919211,0.002496296],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0003185015,0.0002162742,0.02423482,0.001792438,0.0002128371,0.01018753,0.002167229,0.001955176,0.00548129,0.002501711,0.5614487,0.3894834],"study_design_scores_gemma":[0.0002235051,0.0004558608,0.02788213,0.01278463,0.0004742893,0.0209658,0.002729853,0.003694176,0.002834511,0.005414109,0.9222543,0.000286926],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"review","genre_scores_codex":[0.06073154,0.1266028,0.03598293,0.6714644,0.02567432,0.002278791,0.001131364,0.0005283047,0.0756055],"genre_scores_gemma":[0.5339233,0.1061519,0.06518308,0.2476091,0.02195475,0.001906176,0.003283039,0.0002894054,0.01969923],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.01851733,"threshold_uncertainty_score":0.09793019,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.1285376928833178,"score_gpt":0.3375747071494325,"score_spread":0.2090370142661147,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}